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Huge interparietal posterior fontanel meningohydroencephalocele
Congenital encephalocele is a neural tube defect characterized by a sac-like protrusion of the brain, meninges, and other intracranial structures through the skull, which is caused by an embryonic development abnormality. The most common location is at the occipital bone, and its incidence varies ac...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
São Paulo, SP: Universidade de São Paulo, Hospital Universitário
2015
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4608168/ https://www.ncbi.nlm.nih.gov/pubmed/26484324 http://dx.doi.org/10.4322/acr.2014.049 |
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author | Rosildo, Jorge Félix Companioni Dos Santos, Manuel Filipe Dias de Santa Barbara, Rita de Cassia |
author_facet | Rosildo, Jorge Félix Companioni Dos Santos, Manuel Filipe Dias de Santa Barbara, Rita de Cassia |
author_sort | Rosildo, Jorge Félix Companioni |
collection | PubMed |
description | Congenital encephalocele is a neural tube defect characterized by a sac-like protrusion of the brain, meninges, and other intracranial structures through the skull, which is caused by an embryonic development abnormality. The most common location is at the occipital bone, and its incidence varies according to different world regions. We report a case of an 1-month and 7-day-old male child with a huge interparietal-posterior fontanel meningohydroencephalocele, a rare occurrence. Physical examination and volumetric computed tomography were diagnostic. The encephalocele was surgically resected. Intradural and extradural approaches were performed; the bone defect was not primarily closed. Two days after surgery, the patient developed hydrocephaly requiring ventriculoperitoneal shunting. The surgical treatment of the meningohydroencephalocele of the interparietal-posterior fontanel may be accompanied by technical challenges and followed by complications due to the presence of large blood vessels under the overlying skin. In these cases, huge sacs herniate through large bone defects including meninges, brain, and blood vessels. The latter present communication with the superior sagittal sinus and ventricular system. A favorable surgical outcome generally follows an accurate strategy taking into account individual features of the lesion. |
format | Online Article Text |
id | pubmed-4608168 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2015 |
publisher | São Paulo, SP: Universidade de São Paulo, Hospital Universitário |
record_format | MEDLINE/PubMed |
spelling | pubmed-46081682015-10-19 Huge interparietal posterior fontanel meningohydroencephalocele Rosildo, Jorge Félix Companioni Dos Santos, Manuel Filipe Dias de Santa Barbara, Rita de Cassia Autops Case Rep Article / Clinical Case Reports Congenital encephalocele is a neural tube defect characterized by a sac-like protrusion of the brain, meninges, and other intracranial structures through the skull, which is caused by an embryonic development abnormality. The most common location is at the occipital bone, and its incidence varies according to different world regions. We report a case of an 1-month and 7-day-old male child with a huge interparietal-posterior fontanel meningohydroencephalocele, a rare occurrence. Physical examination and volumetric computed tomography were diagnostic. The encephalocele was surgically resected. Intradural and extradural approaches were performed; the bone defect was not primarily closed. Two days after surgery, the patient developed hydrocephaly requiring ventriculoperitoneal shunting. The surgical treatment of the meningohydroencephalocele of the interparietal-posterior fontanel may be accompanied by technical challenges and followed by complications due to the presence of large blood vessels under the overlying skin. In these cases, huge sacs herniate through large bone defects including meninges, brain, and blood vessels. The latter present communication with the superior sagittal sinus and ventricular system. A favorable surgical outcome generally follows an accurate strategy taking into account individual features of the lesion. São Paulo, SP: Universidade de São Paulo, Hospital Universitário 2015-03-30 /pmc/articles/PMC4608168/ /pubmed/26484324 http://dx.doi.org/10.4322/acr.2014.049 Text en Autopsy and Case Reports. ISSN 2236-1960. Copyright © 2014. http://creativecommons.org/licenses/by-nc/3.0/ This is an Open Access article distributed of terms of the Creative Commons Attribution Non-Commercial License which permits unrestricted non-commercial use, distribution, and reproduction in any medium provided article is properly cited. |
spellingShingle | Article / Clinical Case Reports Rosildo, Jorge Félix Companioni Dos Santos, Manuel Filipe Dias de Santa Barbara, Rita de Cassia Huge interparietal posterior fontanel meningohydroencephalocele |
title | Huge interparietal posterior fontanel meningohydroencephalocele |
title_full | Huge interparietal posterior fontanel meningohydroencephalocele |
title_fullStr | Huge interparietal posterior fontanel meningohydroencephalocele |
title_full_unstemmed | Huge interparietal posterior fontanel meningohydroencephalocele |
title_short | Huge interparietal posterior fontanel meningohydroencephalocele |
title_sort | huge interparietal posterior fontanel meningohydroencephalocele |
topic | Article / Clinical Case Reports |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4608168/ https://www.ncbi.nlm.nih.gov/pubmed/26484324 http://dx.doi.org/10.4322/acr.2014.049 |
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