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A Case Report of Vogt's Limbal Girdle and Retinitis Pigmentosa in a Thirteen-Year-Old Boy: A Rare and Unusual Association

AIM: To describe a rare case of Vogt's limbal girdle in a boy with retinitis pigmentosa. METHODS: A 13-year-old boy from India presented to us with progressive diminution of vision and nyctalopia for 5 years. On examination, he had the characteristic features of retinitis pigmentosa with the fu...

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Detalles Bibliográficos
Autores principales: Vignesh, A.P., Srinivasan, Renuka, Karanth, Swathi, Vijitha, Sai
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4608640/
https://www.ncbi.nlm.nih.gov/pubmed/26483674
http://dx.doi.org/10.1159/000439265
Descripción
Sumario:AIM: To describe a rare case of Vogt's limbal girdle in a boy with retinitis pigmentosa. METHODS: A 13-year-old boy from India presented to us with progressive diminution of vision and nyctalopia for 5 years. On examination, he had the characteristic features of retinitis pigmentosa with the fundus showing disc pallor, bony spicules and arteriolar attenuation. His anterior segment examination showed Vogt's limbal girdle in both eyes. RESULTS: Vogt's limbal girdle is a corneal degeneration usually seen in elderly individuals. This is the first time it is seen in association with retinitis pigmentosa. It has also never been reported at such a young age. CONCLUSION: We report a rare case where Vogt's limbal girdle was observed in a 13-year-old boy with retinitis pigmentosa. This gives further insight into the pathogenesis of the disease.