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Congenital cystic adenomatoid malformation type I
Congenital cystic adenomatoid malformation (CCAM) is an hamartomatous congenital pulmonary airway malformation with incidence ranging between 1:10,000 and 1:35,000 newborns. Currently CCAM is classified into five groups according to clinical and pathological features. The clinical outcome varies dep...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
São Paulo, SP: Universidade de São Paulo, Hospital Universitário
2015
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4636102/ https://www.ncbi.nlm.nih.gov/pubmed/26558243 http://dx.doi.org/10.4322/acr.2015.019 |
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author | dos Reis, Alice Rebelo de Matos Borges Ribeiro, Frederico Becker Schultz, Regina |
author_facet | dos Reis, Alice Rebelo de Matos Borges Ribeiro, Frederico Becker Schultz, Regina |
author_sort | dos Reis, Alice Rebelo de Matos Borges |
collection | PubMed |
description | Congenital cystic adenomatoid malformation (CCAM) is an hamartomatous congenital pulmonary airway malformation with incidence ranging between 1:10,000 and 1:35,000 newborns. Currently CCAM is classified into five groups according to clinical and pathological features. The clinical outcome varies depending on the subtype and the extent of involvement. The authors report the case of a premature male newborn with the prenatal diagnosis of CCAM Type 1 associated with cardiac right axis deviation, who died 67 hours after birth due to respiratory failure. In addition to the autopsy report of this rare entity, the authors present its classification and prognosis. |
format | Online Article Text |
id | pubmed-4636102 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2015 |
publisher | São Paulo, SP: Universidade de São Paulo, Hospital Universitário |
record_format | MEDLINE/PubMed |
spelling | pubmed-46361022015-11-10 Congenital cystic adenomatoid malformation type I dos Reis, Alice Rebelo de Matos Borges Ribeiro, Frederico Becker Schultz, Regina Autops Case Rep Article / Autopsy Case Report Congenital cystic adenomatoid malformation (CCAM) is an hamartomatous congenital pulmonary airway malformation with incidence ranging between 1:10,000 and 1:35,000 newborns. Currently CCAM is classified into five groups according to clinical and pathological features. The clinical outcome varies depending on the subtype and the extent of involvement. The authors report the case of a premature male newborn with the prenatal diagnosis of CCAM Type 1 associated with cardiac right axis deviation, who died 67 hours after birth due to respiratory failure. In addition to the autopsy report of this rare entity, the authors present its classification and prognosis. São Paulo, SP: Universidade de São Paulo, Hospital Universitário 2015-09-30 /pmc/articles/PMC4636102/ /pubmed/26558243 http://dx.doi.org/10.4322/acr.2015.019 Text en Autopsy and Case Reports. ISSN 2236-1960. Copyright © 2014. http://creativecommons.org/licenses/by-nc/3.0/ This is an Open Access article distributed of terms of the Creative Commons Attribution Non-Commercial License which permits unrestricted non-commercial use, distribution, and reproduction in any medium provided article is properly cited. |
spellingShingle | Article / Autopsy Case Report dos Reis, Alice Rebelo de Matos Borges Ribeiro, Frederico Becker Schultz, Regina Congenital cystic adenomatoid malformation type I |
title | Congenital cystic adenomatoid malformation type I |
title_full | Congenital cystic adenomatoid malformation type I |
title_fullStr | Congenital cystic adenomatoid malformation type I |
title_full_unstemmed | Congenital cystic adenomatoid malformation type I |
title_short | Congenital cystic adenomatoid malformation type I |
title_sort | congenital cystic adenomatoid malformation type i |
topic | Article / Autopsy Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4636102/ https://www.ncbi.nlm.nih.gov/pubmed/26558243 http://dx.doi.org/10.4322/acr.2015.019 |
work_keys_str_mv | AT dosreisalicerebelodematosborges congenitalcysticadenomatoidmalformationtypei AT ribeirofredericobecker congenitalcysticadenomatoidmalformationtypei AT schultzregina congenitalcysticadenomatoidmalformationtypei |