Testicular Adrenal Rest Tumors (TARTS) With Unusual Histological Features in Congenital Adrenal Hyperplasia (CAH)

Congenital adrenal hyperplasia (CAH) patients with testicular adrenal rest tumors (TARTs) with testicular enlargement present a serious diagnostic challenge. According to the data TARTs are usually benign. They are rare, resulting in paucity in the medical literature regarding their pathological fea...

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Detalles Bibliográficos
Autores principales: Marianovsky, Valeri, Bogdanova, Olga, Tsvetkov, Milen, Serteva, Denitsa, Mladenov, Boris
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2015
Materias:
Congenital Anomalies/Anatomical Variants
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4672664/
https://www.ncbi.nlm.nih.gov/pubmed/26793526
http://dx.doi.org/10.1016/j.eucr.2015.04.008
Descripción
Sumario:Congenital adrenal hyperplasia (CAH) patients with testicular adrenal rest tumors (TARTs) with testicular enlargement present a serious diagnostic challenge. According to the data TARTs are usually benign. They are rare, resulting in paucity in the medical literature regarding their pathological features. We report a case of bilateral synchronous mass-forming TARTs with marked cytological and nuclear atypia misinterpreted as malignant testicular tumors in a 40-years-old man with CAH and CT and MRI data for pheochromocytoma of the right adrenal gland and paraaortal and paracaval lymphadenomegaly. He was previously diagnosed with adrenal cortical carcinoma of the left adrenal gland.

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