Testicular Adrenal Rest Tumors (TARTS) With Unusual Histological Features in Congenital Adrenal Hyperplasia (CAH)

Congenital adrenal hyperplasia (CAH) patients with testicular adrenal rest tumors (TARTs) with testicular enlargement present a serious diagnostic challenge. According to the data TARTs are usually benign. They are rare, resulting in paucity in the medical literature regarding their pathological fea...

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Autores principales: Marianovsky, Valeri, Bogdanova, Olga, Tsvetkov, Milen, Serteva, Denitsa, Mladenov, Boris
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2015
Materias:
Congenital Anomalies/Anatomical Variants
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4672664/
https://www.ncbi.nlm.nih.gov/pubmed/26793526
http://dx.doi.org/10.1016/j.eucr.2015.04.008
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author Marianovsky, Valeri
Bogdanova, Olga
Tsvetkov, Milen
Serteva, Denitsa
Mladenov, Boris
author_facet Marianovsky, Valeri
Bogdanova, Olga
Tsvetkov, Milen
Serteva, Denitsa
Mladenov, Boris
author_sort Marianovsky, Valeri
collection PubMed
description Congenital adrenal hyperplasia (CAH) patients with testicular adrenal rest tumors (TARTs) with testicular enlargement present a serious diagnostic challenge. According to the data TARTs are usually benign. They are rare, resulting in paucity in the medical literature regarding their pathological features. We report a case of bilateral synchronous mass-forming TARTs with marked cytological and nuclear atypia misinterpreted as malignant testicular tumors in a 40-years-old man with CAH and CT and MRI data for pheochromocytoma of the right adrenal gland and paraaortal and paracaval lymphadenomegaly. He was previously diagnosed with adrenal cortical carcinoma of the left adrenal gland.
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spelling pubmed-46726642016-01-20 Testicular Adrenal Rest Tumors (TARTS) With Unusual Histological Features in Congenital Adrenal Hyperplasia (CAH) Marianovsky, Valeri Bogdanova, Olga Tsvetkov, Milen Serteva, Denitsa Mladenov, Boris Urol Case Rep Congenital Anomalies/Anatomical Variants Congenital adrenal hyperplasia (CAH) patients with testicular adrenal rest tumors (TARTs) with testicular enlargement present a serious diagnostic challenge. According to the data TARTs are usually benign. They are rare, resulting in paucity in the medical literature regarding their pathological features. We report a case of bilateral synchronous mass-forming TARTs with marked cytological and nuclear atypia misinterpreted as malignant testicular tumors in a 40-years-old man with CAH and CT and MRI data for pheochromocytoma of the right adrenal gland and paraaortal and paracaval lymphadenomegaly. He was previously diagnosed with adrenal cortical carcinoma of the left adrenal gland. Elsevier 2015-05-27 /pmc/articles/PMC4672664/ /pubmed/26793526 http://dx.doi.org/10.1016/j.eucr.2015.04.008 Text en © 2015 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Congenital Anomalies/Anatomical Variants
Marianovsky, Valeri
Bogdanova, Olga
Tsvetkov, Milen
Serteva, Denitsa
Mladenov, Boris
Testicular Adrenal Rest Tumors (TARTS) With Unusual Histological Features in Congenital Adrenal Hyperplasia (CAH)
title Testicular Adrenal Rest Tumors (TARTS) With Unusual Histological Features in Congenital Adrenal Hyperplasia (CAH)
title_full Testicular Adrenal Rest Tumors (TARTS) With Unusual Histological Features in Congenital Adrenal Hyperplasia (CAH)
title_fullStr Testicular Adrenal Rest Tumors (TARTS) With Unusual Histological Features in Congenital Adrenal Hyperplasia (CAH)
title_full_unstemmed Testicular Adrenal Rest Tumors (TARTS) With Unusual Histological Features in Congenital Adrenal Hyperplasia (CAH)
title_short Testicular Adrenal Rest Tumors (TARTS) With Unusual Histological Features in Congenital Adrenal Hyperplasia (CAH)
title_sort testicular adrenal rest tumors (tarts) with unusual histological features in congenital adrenal hyperplasia (cah)
topic Congenital Anomalies/Anatomical Variants
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4672664/
https://www.ncbi.nlm.nih.gov/pubmed/26793526
http://dx.doi.org/10.1016/j.eucr.2015.04.008
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