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Circadian profiling in two mouse models of lysosomal storage disorders; Niemann Pick type-C and Sandhoff disease
Sleep and circadian rhythm disruption is frequently associated with neurodegenerative disease, yet it is unclear how the specific pathology in these disorders leads to abnormal rest/activity profiles. To investigate whether the pathological features of lysosomal storage disorders (LSDs) influence th...
Autores principales: | Richardson, Katie, Livieratos, Achilleas, Dumbill, Richard, Hughes, Steven, Ang, Gauri, Smith, David A., Morris, Lauren, Brown, Laurence A., Peirson, Stuart N., Platt, Frances M., Davies, Kay E., Oliver, Peter L. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier/North-Holland Biomedical Press
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4678117/ https://www.ncbi.nlm.nih.gov/pubmed/26467605 http://dx.doi.org/10.1016/j.bbr.2015.10.021 |
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