Unilateral, Linear Blue Rubber Bleb Nevus Syndrome (Bean's syndrome): An Unfamiliar Presentation: First Case from India

Blue rubber bleb nevus syndrome (BRBNS) also called Bean's syndrome is a rare disorder characterized by multiple cutaneous venous malformations in association with visceral lesions, most commonly affecting the gastrointestinal tract. We report here, a 21-year-old woman patient, who presented wi...

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Autores principales: Sancheti, Karan, Podder, Indrashis, Das, Anupam, Choudhury, Sourav, Chandra, Somodyuti, Gharami, Ramesh Chandra
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2015
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4681206/
https://www.ncbi.nlm.nih.gov/pubmed/26677281
http://dx.doi.org/10.4103/0019-5154.159644
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author Sancheti, Karan
Podder, Indrashis
Das, Anupam
Choudhury, Sourav
Chandra, Somodyuti
Gharami, Ramesh Chandra
author_facet Sancheti, Karan
Podder, Indrashis
Das, Anupam
Choudhury, Sourav
Chandra, Somodyuti
Gharami, Ramesh Chandra
author_sort Sancheti, Karan
collection PubMed
description Blue rubber bleb nevus syndrome (BRBNS) also called Bean's syndrome is a rare disorder characterized by multiple cutaneous venous malformations in association with visceral lesions, most commonly affecting the gastrointestinal tract. We report here, a 21-year-old woman patient, who presented with unilateral, blaschkoid distribution of cutaneous venous malformations along with blue rubber bleb nevus and recurrent episodes of hematochezia due to vascular lesions in the sigmoid colon; likely to be a case of BRBNS. The unusual unilateral, blaschkoid distribution of BRBNS prompted this present report.
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spelling pubmed-46812062015-12-16 Unilateral, Linear Blue Rubber Bleb Nevus Syndrome (Bean's syndrome): An Unfamiliar Presentation: First Case from India Sancheti, Karan Podder, Indrashis Das, Anupam Choudhury, Sourav Chandra, Somodyuti Gharami, Ramesh Chandra Indian J Dermatol Case Report Blue rubber bleb nevus syndrome (BRBNS) also called Bean's syndrome is a rare disorder characterized by multiple cutaneous venous malformations in association with visceral lesions, most commonly affecting the gastrointestinal tract. We report here, a 21-year-old woman patient, who presented with unilateral, blaschkoid distribution of cutaneous venous malformations along with blue rubber bleb nevus and recurrent episodes of hematochezia due to vascular lesions in the sigmoid colon; likely to be a case of BRBNS. The unusual unilateral, blaschkoid distribution of BRBNS prompted this present report. Medknow Publications & Media Pvt Ltd 2015 /pmc/articles/PMC4681206/ /pubmed/26677281 http://dx.doi.org/10.4103/0019-5154.159644 Text en Copyright: © 2015 Indian Journal of Dermatology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Case Report
Sancheti, Karan
Podder, Indrashis
Das, Anupam
Choudhury, Sourav
Chandra, Somodyuti
Gharami, Ramesh Chandra
Unilateral, Linear Blue Rubber Bleb Nevus Syndrome (Bean's syndrome): An Unfamiliar Presentation: First Case from India
title Unilateral, Linear Blue Rubber Bleb Nevus Syndrome (Bean's syndrome): An Unfamiliar Presentation: First Case from India
title_full Unilateral, Linear Blue Rubber Bleb Nevus Syndrome (Bean's syndrome): An Unfamiliar Presentation: First Case from India
title_fullStr Unilateral, Linear Blue Rubber Bleb Nevus Syndrome (Bean's syndrome): An Unfamiliar Presentation: First Case from India
title_full_unstemmed Unilateral, Linear Blue Rubber Bleb Nevus Syndrome (Bean's syndrome): An Unfamiliar Presentation: First Case from India
title_short Unilateral, Linear Blue Rubber Bleb Nevus Syndrome (Bean's syndrome): An Unfamiliar Presentation: First Case from India
title_sort unilateral, linear blue rubber bleb nevus syndrome (bean's syndrome): an unfamiliar presentation: first case from india
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4681206/
https://www.ncbi.nlm.nih.gov/pubmed/26677281
http://dx.doi.org/10.4103/0019-5154.159644
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