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Hearing rehabilitation in Treacher Collins Syndrome with bone anchored hearing aid

OBJECTIVE: To describe a case of hearing rehabilitation with bone anchored hearing aid in a patient with Treacher Collins syndrome. CASE DESCRIPTION: 3 years old patient, male, with Treacher Collins syndrome and severe complications due to the syndrome, mostly related to the upper airway and hearing...

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Detalles Bibliográficos
Autores principales: Polanski, José Fernando, Plawiak, Anna Clara, Ribas, Angela
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade de Pediatria de São Paulo 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4685570/
https://www.ncbi.nlm.nih.gov/pubmed/26298651
http://dx.doi.org/10.1016/j.rpped.2015.01.010
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author Polanski, José Fernando
Plawiak, Anna Clara
Ribas, Angela
author_facet Polanski, José Fernando
Plawiak, Anna Clara
Ribas, Angela
author_sort Polanski, José Fernando
collection PubMed
description OBJECTIVE: To describe a case of hearing rehabilitation with bone anchored hearing aid in a patient with Treacher Collins syndrome. CASE DESCRIPTION: 3 years old patient, male, with Treacher Collins syndrome and severe complications due to the syndrome, mostly related to the upper airway and hearing. He had bilateral atresia of external auditory canals, and malformation of the pinna. The initial hearing rehabilitation was with bone vibration arch, but there was poor acceptance due the discomfort caused by skull compression. It was prescribed a model of bone-anchored hearing aid, in soft band format. The results were evaluated through behavioral hearing tests and questionnaires Meaningful Use of Speech Scale (MUSS) and Infant-Toddler Meaningful Auditory Integration Scale (IT-MAIS). COMMENTS: The patient had a higher acceptance of the bone-anchored hearing aid compared to the traditional bone vibration arch. Audiological tests and the speech and auditory skills assessments also showed better communication and hearing outcomes. The bone-anchored hearing aid is a good option in hearing rehabilitation in this syndrome.
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spelling pubmed-46855702015-12-29 Hearing rehabilitation in Treacher Collins Syndrome with bone anchored hearing aid Polanski, José Fernando Plawiak, Anna Clara Ribas, Angela Rev Paul Pediatr Case Reports OBJECTIVE: To describe a case of hearing rehabilitation with bone anchored hearing aid in a patient with Treacher Collins syndrome. CASE DESCRIPTION: 3 years old patient, male, with Treacher Collins syndrome and severe complications due to the syndrome, mostly related to the upper airway and hearing. He had bilateral atresia of external auditory canals, and malformation of the pinna. The initial hearing rehabilitation was with bone vibration arch, but there was poor acceptance due the discomfort caused by skull compression. It was prescribed a model of bone-anchored hearing aid, in soft band format. The results were evaluated through behavioral hearing tests and questionnaires Meaningful Use of Speech Scale (MUSS) and Infant-Toddler Meaningful Auditory Integration Scale (IT-MAIS). COMMENTS: The patient had a higher acceptance of the bone-anchored hearing aid compared to the traditional bone vibration arch. Audiological tests and the speech and auditory skills assessments also showed better communication and hearing outcomes. The bone-anchored hearing aid is a good option in hearing rehabilitation in this syndrome. Sociedade de Pediatria de São Paulo 2015 /pmc/articles/PMC4685570/ /pubmed/26298651 http://dx.doi.org/10.1016/j.rpped.2015.01.010 Text en © 2015 Sociedade de Pediatria de São Paulo. Published by Elsevier Editora Ltda http://creativecommons.org/licenses/by/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Reports
Polanski, José Fernando
Plawiak, Anna Clara
Ribas, Angela
Hearing rehabilitation in Treacher Collins Syndrome with bone anchored hearing aid
title Hearing rehabilitation in Treacher Collins Syndrome with bone anchored hearing aid
title_full Hearing rehabilitation in Treacher Collins Syndrome with bone anchored hearing aid
title_fullStr Hearing rehabilitation in Treacher Collins Syndrome with bone anchored hearing aid
title_full_unstemmed Hearing rehabilitation in Treacher Collins Syndrome with bone anchored hearing aid
title_short Hearing rehabilitation in Treacher Collins Syndrome with bone anchored hearing aid
title_sort hearing rehabilitation in treacher collins syndrome with bone anchored hearing aid
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4685570/
https://www.ncbi.nlm.nih.gov/pubmed/26298651
http://dx.doi.org/10.1016/j.rpped.2015.01.010
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