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Non-Trigger Anesthesia Management in a Patient With Leigh’s Syndrome Presenting for Dental Rehabilitation

INTRODUCTION: Usually presenting in infancy, Leigh’s syndrome is an inherited condition often manifesting with seizures, ataxia, developmental delay, and dysarthria. The disorder is rare, appearing in approximately 1 in 40,000 live births. Consequently, providing these patients with a suitable plan...

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Detalles Bibliográficos
Autores principales: Suleman, M-Irfan, Edala, Thejovathi, Abraham, Edwin, Siddiqu, M-Saif
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Kowsar 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4688816/
https://www.ncbi.nlm.nih.gov/pubmed/26705519
http://dx.doi.org/10.5812/aapm.28804
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author Suleman, M-Irfan
Edala, Thejovathi
Abraham, Edwin
Siddiqu, M-Saif
author_facet Suleman, M-Irfan
Edala, Thejovathi
Abraham, Edwin
Siddiqu, M-Saif
author_sort Suleman, M-Irfan
collection PubMed
description INTRODUCTION: Usually presenting in infancy, Leigh’s syndrome is an inherited condition often manifesting with seizures, ataxia, developmental delay, and dysarthria. The disorder is rare, appearing in approximately 1 in 40,000 live births. Consequently, providing these patients with a suitable plan by which to administer anesthetics remains problematic. CASE PRESENTATION: We report a male patient with Leigh’s syndrome and a family history suggestive of unknown hypotonia and malignant hyperthermia presenting for dental rehabilitation. CONCLUSIONS: Dexmedetomidine with remifentanil can be used with no complication in this senerio.
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spelling pubmed-46888162015-12-24 Non-Trigger Anesthesia Management in a Patient With Leigh’s Syndrome Presenting for Dental Rehabilitation Suleman, M-Irfan Edala, Thejovathi Abraham, Edwin Siddiqu, M-Saif Anesth Pain Med Case Report INTRODUCTION: Usually presenting in infancy, Leigh’s syndrome is an inherited condition often manifesting with seizures, ataxia, developmental delay, and dysarthria. The disorder is rare, appearing in approximately 1 in 40,000 live births. Consequently, providing these patients with a suitable plan by which to administer anesthetics remains problematic. CASE PRESENTATION: We report a male patient with Leigh’s syndrome and a family history suggestive of unknown hypotonia and malignant hyperthermia presenting for dental rehabilitation. CONCLUSIONS: Dexmedetomidine with remifentanil can be used with no complication in this senerio. Kowsar 2015-11-30 /pmc/articles/PMC4688816/ /pubmed/26705519 http://dx.doi.org/10.5812/aapm.28804 Text en Copyright © 2015, Iranian Society of Regional Anesthesia and Pain Medicine (ISRAPM). http://creativecommons.org/licenses/by-nc/4.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 International License (http://creativecommons.org/licenses/by-nc/4.0/) which permits copy and redistribute the material just in noncommercial usages, provided the original work is properly cited.
spellingShingle Case Report
Suleman, M-Irfan
Edala, Thejovathi
Abraham, Edwin
Siddiqu, M-Saif
Non-Trigger Anesthesia Management in a Patient With Leigh’s Syndrome Presenting for Dental Rehabilitation
title Non-Trigger Anesthesia Management in a Patient With Leigh’s Syndrome Presenting for Dental Rehabilitation
title_full Non-Trigger Anesthesia Management in a Patient With Leigh’s Syndrome Presenting for Dental Rehabilitation
title_fullStr Non-Trigger Anesthesia Management in a Patient With Leigh’s Syndrome Presenting for Dental Rehabilitation
title_full_unstemmed Non-Trigger Anesthesia Management in a Patient With Leigh’s Syndrome Presenting for Dental Rehabilitation
title_short Non-Trigger Anesthesia Management in a Patient With Leigh’s Syndrome Presenting for Dental Rehabilitation
title_sort non-trigger anesthesia management in a patient with leigh’s syndrome presenting for dental rehabilitation
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4688816/
https://www.ncbi.nlm.nih.gov/pubmed/26705519
http://dx.doi.org/10.5812/aapm.28804
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