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Genetic predisposition to hemophagocytic lymphohistiocytosis: Report on 500 patients from the Italian registry
BACKGROUND: Hemophagocytic lymphohistiocytosis (HLH) is a rare life-threatening disease affecting mostly children but also adults and characterized by hyperinflammatory features. A subset of patients, referred to as having familial hemophagocytic lymphohistiocytosis (FHL), have various underlying ge...
Autores principales: | Cetica, Valentina, Sieni, Elena, Pende, Daniela, Danesino, Cesare, De Fusco, Carmen, Locatelli, Franco, Micalizzi, Concetta, Putti, Maria Caterina, Biondi, Andrea, Fagioli, Franca, Moretta, Lorenzo, Griffiths, Gillian M., Luzzatto, Lucio, Aricò, Maurizio |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Mosby
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4699615/ https://www.ncbi.nlm.nih.gov/pubmed/26342526 http://dx.doi.org/10.1016/j.jaci.2015.06.048 |
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