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Proteus syndrome: evaluation of the immunological profile

Proteus syndrome (PS) is an extremely rare and complex disease characterized by malformations and overgrowth of different tissues. Prognosis of affected patients may be complicated by premature death, mostly due to pulmonary embolism and respiratory failure. To date, immunological data in Proteus sy...

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Detalles Bibliográficos
Autores principales: Lougaris, Vassilios, Salpietro, Vincenzo, Cutrupi, Maricia, Baronio, Manuela, Moratto, Daniele, Pizzino, M. R., Mankad, Kshitij, Briuglia, Silvana, Salpietro, Carmelo, Plebani, Alessandro
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4711050/
https://www.ncbi.nlm.nih.gov/pubmed/26758562
http://dx.doi.org/10.1186/s13023-015-0381-z