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Mitochondrial dysfunction in fatty acid oxidation disorders: insights from human and animal studies

Mitochondrial fatty acid oxidation (FAO) plays a pivotal role in maintaining body energy homoeostasis mainly during catabolic states. Oxidation of fatty acids requires approximately 25 proteins. Inherited defects of FAO have been identified in the majority of these proteins and constitute an importa...

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Detalles Bibliográficos
Autores principales:	Wajner, Moacir, Amaral, Alexandre Umpierrez
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Portland Press Ltd. 2016
Materias:	Review Articles
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4718505/ https://www.ncbi.nlm.nih.gov/pubmed/26589966 http://dx.doi.org/10.1042/BSR20150240

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