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Neuromuscular Junctions as Key Contributors and Therapeutic Targets in Spinal Muscular Atrophy
Spinal muscular atrophy (SMA) is a recessive autosomal neuromuscular disease, representing the most common fatal pediatric pathology. Even though, classically and in a simplistic way, it is categorized as a motor neuron (MN) disease, there is an increasing general consensus that its pathogenesis is...
Autores principales: | Boido, Marina, Vercelli, Alessandro |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4737916/ https://www.ncbi.nlm.nih.gov/pubmed/26869891 http://dx.doi.org/10.3389/fnana.2016.00006 |
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