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Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia

Fibrocartilaginous dysplasia (FCD) is a rare variant of fibrous dysplasia (FD) which frequently involves the long bones, and the proximal femur is the most commonly affected site. This benign, lytic, and expansile bone lesion causes progressive deformity in the bones and may lead to pathological fra...

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Autores principales: Vaishya, Raju, Agarwal, Amit Kumar, Gupta, Nishint, Vijay, Vipul
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4744070/
https://www.ncbi.nlm.nih.gov/pubmed/26918216
http://dx.doi.org/10.7759/cureus.448
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author Vaishya, Raju
Agarwal, Amit Kumar
Gupta, Nishint
Vijay, Vipul
author_facet Vaishya, Raju
Agarwal, Amit Kumar
Gupta, Nishint
Vijay, Vipul
author_sort Vaishya, Raju
collection PubMed
description Fibrocartilaginous dysplasia (FCD) is a rare variant of fibrous dysplasia (FD) which frequently involves the long bones, and the proximal femur is the most commonly affected site. This benign, lytic, and expansile bone lesion causes progressive deformity in the bones and may lead to pathological fracture. Radiologically, this lesion may mimic cartilaginous benign and malignant bone tumors. Therefore, histopathological differentiation of FCD from other cartilaginous tumors is of the utmost importance. The treatment is often surgical, in the form of curettage and bone grafting or corrective osteotomy, to treat progressive deformity in the long bones. The risk of pathological fracture is high in FCD with bony deformity and often requires surgery.
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spelling pubmed-47440702016-02-25 Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia Vaishya, Raju Agarwal, Amit Kumar Gupta, Nishint Vijay, Vipul Cureus Pathology Fibrocartilaginous dysplasia (FCD) is a rare variant of fibrous dysplasia (FD) which frequently involves the long bones, and the proximal femur is the most commonly affected site. This benign, lytic, and expansile bone lesion causes progressive deformity in the bones and may lead to pathological fracture. Radiologically, this lesion may mimic cartilaginous benign and malignant bone tumors. Therefore, histopathological differentiation of FCD from other cartilaginous tumors is of the utmost importance. The treatment is often surgical, in the form of curettage and bone grafting or corrective osteotomy, to treat progressive deformity in the long bones. The risk of pathological fracture is high in FCD with bony deformity and often requires surgery. Cureus 2016-01-05 /pmc/articles/PMC4744070/ /pubmed/26918216 http://dx.doi.org/10.7759/cureus.448 Text en Copyright © 2016, Vaishya et al. http://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Pathology
Vaishya, Raju
Agarwal, Amit Kumar
Gupta, Nishint
Vijay, Vipul
Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia
title Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia
title_full Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia
title_fullStr Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia
title_full_unstemmed Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia
title_short Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia
title_sort fibrocartilaginous dysplasia of the bone: a rare variant of fibrous dysplasia
topic Pathology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4744070/
https://www.ncbi.nlm.nih.gov/pubmed/26918216
http://dx.doi.org/10.7759/cureus.448
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