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Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia
Fibrocartilaginous dysplasia (FCD) is a rare variant of fibrous dysplasia (FD) which frequently involves the long bones, and the proximal femur is the most commonly affected site. This benign, lytic, and expansile bone lesion causes progressive deformity in the bones and may lead to pathological fra...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Cureus
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4744070/ https://www.ncbi.nlm.nih.gov/pubmed/26918216 http://dx.doi.org/10.7759/cureus.448 |
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author | Vaishya, Raju Agarwal, Amit Kumar Gupta, Nishint Vijay, Vipul |
author_facet | Vaishya, Raju Agarwal, Amit Kumar Gupta, Nishint Vijay, Vipul |
author_sort | Vaishya, Raju |
collection | PubMed |
description | Fibrocartilaginous dysplasia (FCD) is a rare variant of fibrous dysplasia (FD) which frequently involves the long bones, and the proximal femur is the most commonly affected site. This benign, lytic, and expansile bone lesion causes progressive deformity in the bones and may lead to pathological fracture. Radiologically, this lesion may mimic cartilaginous benign and malignant bone tumors. Therefore, histopathological differentiation of FCD from other cartilaginous tumors is of the utmost importance. The treatment is often surgical, in the form of curettage and bone grafting or corrective osteotomy, to treat progressive deformity in the long bones. The risk of pathological fracture is high in FCD with bony deformity and often requires surgery. |
format | Online Article Text |
id | pubmed-4744070 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Cureus |
record_format | MEDLINE/PubMed |
spelling | pubmed-47440702016-02-25 Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia Vaishya, Raju Agarwal, Amit Kumar Gupta, Nishint Vijay, Vipul Cureus Pathology Fibrocartilaginous dysplasia (FCD) is a rare variant of fibrous dysplasia (FD) which frequently involves the long bones, and the proximal femur is the most commonly affected site. This benign, lytic, and expansile bone lesion causes progressive deformity in the bones and may lead to pathological fracture. Radiologically, this lesion may mimic cartilaginous benign and malignant bone tumors. Therefore, histopathological differentiation of FCD from other cartilaginous tumors is of the utmost importance. The treatment is often surgical, in the form of curettage and bone grafting or corrective osteotomy, to treat progressive deformity in the long bones. The risk of pathological fracture is high in FCD with bony deformity and often requires surgery. Cureus 2016-01-05 /pmc/articles/PMC4744070/ /pubmed/26918216 http://dx.doi.org/10.7759/cureus.448 Text en Copyright © 2016, Vaishya et al. http://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. |
spellingShingle | Pathology Vaishya, Raju Agarwal, Amit Kumar Gupta, Nishint Vijay, Vipul Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia |
title | Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia |
title_full | Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia |
title_fullStr | Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia |
title_full_unstemmed | Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia |
title_short | Fibrocartilaginous Dysplasia of the Bone: A Rare Variant of Fibrous Dysplasia |
title_sort | fibrocartilaginous dysplasia of the bone: a rare variant of fibrous dysplasia |
topic | Pathology |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4744070/ https://www.ncbi.nlm.nih.gov/pubmed/26918216 http://dx.doi.org/10.7759/cureus.448 |
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