Perisigmoid Abscess Leading to a Diagnosis of Ehlers-Danlos Syndrome Type IV

The Ehlers-Danlos syndromes (EDS) are a group of connective tissue disorders characterized by triad of joint hypermobility, skin extensibility, and tissue fragility. Ehlers-Danlos syndrome type IV places patients at risk for life-threatening, spontaneous, vascular or visceral rupture due to reduced...

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Autores principales: Normatov, Inessa, Kesavan, Anil, Srikumar, Pillai B., McConnie, Randolph M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: American College of Gastroenterology 2016
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4748196/
https://www.ncbi.nlm.nih.gov/pubmed/26958560
http://dx.doi.org/10.14309/crj.2016.14
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author Normatov, Inessa
Kesavan, Anil
Srikumar, Pillai B.
McConnie, Randolph M.
author_facet Normatov, Inessa
Kesavan, Anil
Srikumar, Pillai B.
McConnie, Randolph M.
author_sort Normatov, Inessa
collection PubMed
description The Ehlers-Danlos syndromes (EDS) are a group of connective tissue disorders characterized by triad of joint hypermobility, skin extensibility, and tissue fragility. Ehlers-Danlos syndrome type IV places patients at risk for life-threatening, spontaneous, vascular or visceral rupture due to reduced or abnormal secretion of type III collagen. We present an adolescent male who was found to have a perisigmoid abscess with a fistula connecting to adjacent sigmoid colon secondary to undiagnosed EDS type IV. Conservative management with antibiotics and bowel rest was pursued to allow for elective resection for his acute complicated diverticulitis at a safer time.
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spelling pubmed-47481962016-03-08 Perisigmoid Abscess Leading to a Diagnosis of Ehlers-Danlos Syndrome Type IV Normatov, Inessa Kesavan, Anil Srikumar, Pillai B. McConnie, Randolph M. ACG Case Rep J Case Report The Ehlers-Danlos syndromes (EDS) are a group of connective tissue disorders characterized by triad of joint hypermobility, skin extensibility, and tissue fragility. Ehlers-Danlos syndrome type IV places patients at risk for life-threatening, spontaneous, vascular or visceral rupture due to reduced or abnormal secretion of type III collagen. We present an adolescent male who was found to have a perisigmoid abscess with a fistula connecting to adjacent sigmoid colon secondary to undiagnosed EDS type IV. Conservative management with antibiotics and bowel rest was pursued to allow for elective resection for his acute complicated diverticulitis at a safer time. American College of Gastroenterology 2016-01-20 /pmc/articles/PMC4748196/ /pubmed/26958560 http://dx.doi.org/10.14309/crj.2016.14 Text en Copyright © Normatov et al. This is an open-access article. This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. To view a copy of this license, visit http://creativecommons.org/licenses/by-nc-nd/4.0/
spellingShingle Case Report
Normatov, Inessa
Kesavan, Anil
Srikumar, Pillai B.
McConnie, Randolph M.
Perisigmoid Abscess Leading to a Diagnosis of Ehlers-Danlos Syndrome Type IV
title Perisigmoid Abscess Leading to a Diagnosis of Ehlers-Danlos Syndrome Type IV
title_full Perisigmoid Abscess Leading to a Diagnosis of Ehlers-Danlos Syndrome Type IV
title_fullStr Perisigmoid Abscess Leading to a Diagnosis of Ehlers-Danlos Syndrome Type IV
title_full_unstemmed Perisigmoid Abscess Leading to a Diagnosis of Ehlers-Danlos Syndrome Type IV
title_short Perisigmoid Abscess Leading to a Diagnosis of Ehlers-Danlos Syndrome Type IV
title_sort perisigmoid abscess leading to a diagnosis of ehlers-danlos syndrome type iv
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4748196/
https://www.ncbi.nlm.nih.gov/pubmed/26958560
http://dx.doi.org/10.14309/crj.2016.14
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