A rare form of cardiomyopathy: left ventricular non-compaction cardiomyopathy

Left ventricular non-compaction is a recently recognized, rare form of cardiomyopathy. It is based on the arrest of endomyocardial morphogenesis during embryogenesis. It was first described in 1984 by Engberding who described it as isolated ‘sinusoids’ within the LV. Right now its prevalence is esti...

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Detalles Bibliográficos
Autores principales: Goud, Aditya, Padmanabhan, Sriram
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Co-Action Publishing 2016
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4763555/
https://www.ncbi.nlm.nih.gov/pubmed/26908378
http://dx.doi.org/10.3402/jchimp.v6.29888
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author Goud, Aditya
Padmanabhan, Sriram
author_facet Goud, Aditya
Padmanabhan, Sriram
author_sort Goud, Aditya
collection PubMed
description Left ventricular non-compaction is a recently recognized, rare form of cardiomyopathy. It is based on the arrest of endomyocardial morphogenesis during embryogenesis. It was first described in 1984 by Engberding who described it as isolated ‘sinusoids’ within the LV. Right now its prevalence is estimated at 0.014 to 1.3 and 3–4% in heart failure patients. Its clinical manifestations are highly variable, ranging from no symptoms to disabling congestive heart failure, arrhythmias, and systemic thromboemboli. Doppler Echocardiogram is considered the diagnostic procedure of choice and treatment is symptomatic management of its symptoms and complications.
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spelling pubmed-47635552016-03-09 A rare form of cardiomyopathy: left ventricular non-compaction cardiomyopathy Goud, Aditya Padmanabhan, Sriram J Community Hosp Intern Med Perspect Case Report Left ventricular non-compaction is a recently recognized, rare form of cardiomyopathy. It is based on the arrest of endomyocardial morphogenesis during embryogenesis. It was first described in 1984 by Engberding who described it as isolated ‘sinusoids’ within the LV. Right now its prevalence is estimated at 0.014 to 1.3 and 3–4% in heart failure patients. Its clinical manifestations are highly variable, ranging from no symptoms to disabling congestive heart failure, arrhythmias, and systemic thromboemboli. Doppler Echocardiogram is considered the diagnostic procedure of choice and treatment is symptomatic management of its symptoms and complications. Co-Action Publishing 2016-02-17 /pmc/articles/PMC4763555/ /pubmed/26908378 http://dx.doi.org/10.3402/jchimp.v6.29888 Text en © 2016 Aditya Goud and Sriram Padmanabhan http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 International License, permitting all non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Goud, Aditya
Padmanabhan, Sriram
A rare form of cardiomyopathy: left ventricular non-compaction cardiomyopathy
title A rare form of cardiomyopathy: left ventricular non-compaction cardiomyopathy
title_full A rare form of cardiomyopathy: left ventricular non-compaction cardiomyopathy
title_fullStr A rare form of cardiomyopathy: left ventricular non-compaction cardiomyopathy
title_full_unstemmed A rare form of cardiomyopathy: left ventricular non-compaction cardiomyopathy
title_short A rare form of cardiomyopathy: left ventricular non-compaction cardiomyopathy
title_sort rare form of cardiomyopathy: left ventricular non-compaction cardiomyopathy
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4763555/
https://www.ncbi.nlm.nih.gov/pubmed/26908378
http://dx.doi.org/10.3402/jchimp.v6.29888
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