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Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells

In this first‐in‐literature case, we describe a patient with Systemic mastocytosis presenting with life‐threatening cardiac tamponade associated with the presence of aberrant mast cells in the pericardium. Procedures involving surgical incisions through the pericardium in such cases can lead to unco...

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Autores principales: Sukrithan, Vineeth K., Salamon, Jason N., Berulava, Giorgi, Sibinga, Nicholas E., Verma, Amit
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4771862/
https://www.ncbi.nlm.nih.gov/pubmed/27014452
http://dx.doi.org/10.1002/ccr3.505
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author Sukrithan, Vineeth K.
Salamon, Jason N.
Berulava, Giorgi
Sibinga, Nicholas E.
Verma, Amit
author_facet Sukrithan, Vineeth K.
Salamon, Jason N.
Berulava, Giorgi
Sibinga, Nicholas E.
Verma, Amit
author_sort Sukrithan, Vineeth K.
collection PubMed
description In this first‐in‐literature case, we describe a patient with Systemic mastocytosis presenting with life‐threatening cardiac tamponade associated with the presence of aberrant mast cells in the pericardium. Procedures involving surgical incisions through the pericardium in such cases can lead to uncontrolled mast cell degranulation leading to circulatory collapse.
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spelling pubmed-47718622016-03-24 Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells Sukrithan, Vineeth K. Salamon, Jason N. Berulava, Giorgi Sibinga, Nicholas E. Verma, Amit Clin Case Rep Case Reports In this first‐in‐literature case, we describe a patient with Systemic mastocytosis presenting with life‐threatening cardiac tamponade associated with the presence of aberrant mast cells in the pericardium. Procedures involving surgical incisions through the pericardium in such cases can lead to uncontrolled mast cell degranulation leading to circulatory collapse. John Wiley and Sons Inc. 2016-02-08 /pmc/articles/PMC4771862/ /pubmed/27014452 http://dx.doi.org/10.1002/ccr3.505 Text en © 2016 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. This is an open access article under the terms of the Creative Commons Attribution‐NonCommercial‐NoDerivs (http://creativecommons.org/licenses/by-nc-nd/4.0/) License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non‐commercial and no modifications or adaptations are made.
spellingShingle Case Reports
Sukrithan, Vineeth K.
Salamon, Jason N.
Berulava, Giorgi
Sibinga, Nicholas E.
Verma, Amit
Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells
title Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells
title_full Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells
title_fullStr Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells
title_full_unstemmed Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells
title_short Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells
title_sort systemic mastocytosis presenting as cardiac tamponade with cd25(+) pericardial mast cells
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4771862/
https://www.ncbi.nlm.nih.gov/pubmed/27014452
http://dx.doi.org/10.1002/ccr3.505
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