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Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells
In this first‐in‐literature case, we describe a patient with Systemic mastocytosis presenting with life‐threatening cardiac tamponade associated with the presence of aberrant mast cells in the pericardium. Procedures involving surgical incisions through the pericardium in such cases can lead to unco...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley and Sons Inc.
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4771862/ https://www.ncbi.nlm.nih.gov/pubmed/27014452 http://dx.doi.org/10.1002/ccr3.505 |
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author | Sukrithan, Vineeth K. Salamon, Jason N. Berulava, Giorgi Sibinga, Nicholas E. Verma, Amit |
author_facet | Sukrithan, Vineeth K. Salamon, Jason N. Berulava, Giorgi Sibinga, Nicholas E. Verma, Amit |
author_sort | Sukrithan, Vineeth K. |
collection | PubMed |
description | In this first‐in‐literature case, we describe a patient with Systemic mastocytosis presenting with life‐threatening cardiac tamponade associated with the presence of aberrant mast cells in the pericardium. Procedures involving surgical incisions through the pericardium in such cases can lead to uncontrolled mast cell degranulation leading to circulatory collapse. |
format | Online Article Text |
id | pubmed-4771862 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | John Wiley and Sons Inc. |
record_format | MEDLINE/PubMed |
spelling | pubmed-47718622016-03-24 Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells Sukrithan, Vineeth K. Salamon, Jason N. Berulava, Giorgi Sibinga, Nicholas E. Verma, Amit Clin Case Rep Case Reports In this first‐in‐literature case, we describe a patient with Systemic mastocytosis presenting with life‐threatening cardiac tamponade associated with the presence of aberrant mast cells in the pericardium. Procedures involving surgical incisions through the pericardium in such cases can lead to uncontrolled mast cell degranulation leading to circulatory collapse. John Wiley and Sons Inc. 2016-02-08 /pmc/articles/PMC4771862/ /pubmed/27014452 http://dx.doi.org/10.1002/ccr3.505 Text en © 2016 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. This is an open access article under the terms of the Creative Commons Attribution‐NonCommercial‐NoDerivs (http://creativecommons.org/licenses/by-nc-nd/4.0/) License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non‐commercial and no modifications or adaptations are made. |
spellingShingle | Case Reports Sukrithan, Vineeth K. Salamon, Jason N. Berulava, Giorgi Sibinga, Nicholas E. Verma, Amit Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells |
title | Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells |
title_full | Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells |
title_fullStr | Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells |
title_full_unstemmed | Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells |
title_short | Systemic mastocytosis presenting as cardiac tamponade with CD25(+) pericardial mast cells |
title_sort | systemic mastocytosis presenting as cardiac tamponade with cd25(+) pericardial mast cells |
topic | Case Reports |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4771862/ https://www.ncbi.nlm.nih.gov/pubmed/27014452 http://dx.doi.org/10.1002/ccr3.505 |
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