Cargando…
Percutaneous Mitral Valvotomy in a Case of Situs Inversus Totalis and Juvenile Rheumatic Critical Mitral Stenosis: Case Report
Situs inversus totalis is a rare congenital disorder where the heart being a mirror image is situated on the right side of the body. Distorted cardiac anatomy makes fluoroscopy-guided percutaneous mitral valvotomy (PMV) technically challenging and there are only few reports of PMV in situs inversus...
Autores principales: | , , , , , , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elmer Press
2016
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4780502/ https://www.ncbi.nlm.nih.gov/pubmed/26985259 http://dx.doi.org/10.14740/jocmr2473w |
_version_ | 1782419776852721664 |
---|---|
author | Sinha, Santosh Kumar Thakur, Ramesh Jha, Mukesh Jitendra Sayal, Karandeep Singh Sachan, Mohit Krishna, Vinay Kumar, Ashutosh Mishra, Vikas Varma, Chandra Mohan |
author_facet | Sinha, Santosh Kumar Thakur, Ramesh Jha, Mukesh Jitendra Sayal, Karandeep Singh Sachan, Mohit Krishna, Vinay Kumar, Ashutosh Mishra, Vikas Varma, Chandra Mohan |
author_sort | Sinha, Santosh Kumar |
collection | PubMed |
description | Situs inversus totalis is a rare congenital disorder where the heart being a mirror image is situated on the right side of the body. Distorted cardiac anatomy makes fluoroscopy-guided percutaneous mitral valvotomy (PMV) technically challenging and there are only few reports of PMV in situs inversus totalis. Here we report a case where PMV was successfully done for situs inversus totalis with rare coincidence of juvenile rheumatic severe mitral stenosis in a 12-year-old boy with a few modifications of standard Inoue technique. He had exertional dyspnea of NYHA class III with initial mitral valve area (MVA) of 0.6 cm(2) and severe pulmonary arterial hypertension with features suitable for PMV. Femoral vein was accessed from the left side to align the septal puncture needle and balloon to facilitate left ventricular entry. Septal descent and puncture by Brockenbrough needle was performed in the right anterior oblique view with the needle facing 5 o’clock position. Accura balloon was negotiated across mitral valve in left anterior oblique and procedure was successfully executed. Echocardiography showed a well-divided anterior commissure with an MVA of 2.0 cm(2) and mild mitral regurgitation. In summary, PMV is safe and feasible in the rare patient with situs inversus totalis with few modifications of the Inoue technique. |
format | Online Article Text |
id | pubmed-4780502 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Elmer Press |
record_format | MEDLINE/PubMed |
spelling | pubmed-47805022016-03-16 Percutaneous Mitral Valvotomy in a Case of Situs Inversus Totalis and Juvenile Rheumatic Critical Mitral Stenosis: Case Report Sinha, Santosh Kumar Thakur, Ramesh Jha, Mukesh Jitendra Sayal, Karandeep Singh Sachan, Mohit Krishna, Vinay Kumar, Ashutosh Mishra, Vikas Varma, Chandra Mohan J Clin Med Res Case Report Situs inversus totalis is a rare congenital disorder where the heart being a mirror image is situated on the right side of the body. Distorted cardiac anatomy makes fluoroscopy-guided percutaneous mitral valvotomy (PMV) technically challenging and there are only few reports of PMV in situs inversus totalis. Here we report a case where PMV was successfully done for situs inversus totalis with rare coincidence of juvenile rheumatic severe mitral stenosis in a 12-year-old boy with a few modifications of standard Inoue technique. He had exertional dyspnea of NYHA class III with initial mitral valve area (MVA) of 0.6 cm(2) and severe pulmonary arterial hypertension with features suitable for PMV. Femoral vein was accessed from the left side to align the septal puncture needle and balloon to facilitate left ventricular entry. Septal descent and puncture by Brockenbrough needle was performed in the right anterior oblique view with the needle facing 5 o’clock position. Accura balloon was negotiated across mitral valve in left anterior oblique and procedure was successfully executed. Echocardiography showed a well-divided anterior commissure with an MVA of 2.0 cm(2) and mild mitral regurgitation. In summary, PMV is safe and feasible in the rare patient with situs inversus totalis with few modifications of the Inoue technique. Elmer Press 2016-04 2016-02-27 /pmc/articles/PMC4780502/ /pubmed/26985259 http://dx.doi.org/10.14740/jocmr2473w Text en Copyright 2016, Sinha et al. http://creativecommons.org/licenses/by/2.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Sinha, Santosh Kumar Thakur, Ramesh Jha, Mukesh Jitendra Sayal, Karandeep Singh Sachan, Mohit Krishna, Vinay Kumar, Ashutosh Mishra, Vikas Varma, Chandra Mohan Percutaneous Mitral Valvotomy in a Case of Situs Inversus Totalis and Juvenile Rheumatic Critical Mitral Stenosis: Case Report |
title | Percutaneous Mitral Valvotomy in a Case of Situs Inversus Totalis and Juvenile Rheumatic Critical Mitral Stenosis: Case Report |
title_full | Percutaneous Mitral Valvotomy in a Case of Situs Inversus Totalis and Juvenile Rheumatic Critical Mitral Stenosis: Case Report |
title_fullStr | Percutaneous Mitral Valvotomy in a Case of Situs Inversus Totalis and Juvenile Rheumatic Critical Mitral Stenosis: Case Report |
title_full_unstemmed | Percutaneous Mitral Valvotomy in a Case of Situs Inversus Totalis and Juvenile Rheumatic Critical Mitral Stenosis: Case Report |
title_short | Percutaneous Mitral Valvotomy in a Case of Situs Inversus Totalis and Juvenile Rheumatic Critical Mitral Stenosis: Case Report |
title_sort | percutaneous mitral valvotomy in a case of situs inversus totalis and juvenile rheumatic critical mitral stenosis: case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4780502/ https://www.ncbi.nlm.nih.gov/pubmed/26985259 http://dx.doi.org/10.14740/jocmr2473w |
work_keys_str_mv | AT sinhasantoshkumar percutaneousmitralvalvotomyinacaseofsitusinversustotalisandjuvenilerheumaticcriticalmitralstenosiscasereport AT thakurramesh percutaneousmitralvalvotomyinacaseofsitusinversustotalisandjuvenilerheumaticcriticalmitralstenosiscasereport AT jhamukeshjitendra percutaneousmitralvalvotomyinacaseofsitusinversustotalisandjuvenilerheumaticcriticalmitralstenosiscasereport AT sayalkarandeepsingh percutaneousmitralvalvotomyinacaseofsitusinversustotalisandjuvenilerheumaticcriticalmitralstenosiscasereport AT sachanmohit percutaneousmitralvalvotomyinacaseofsitusinversustotalisandjuvenilerheumaticcriticalmitralstenosiscasereport AT krishnavinay percutaneousmitralvalvotomyinacaseofsitusinversustotalisandjuvenilerheumaticcriticalmitralstenosiscasereport AT kumarashutosh percutaneousmitralvalvotomyinacaseofsitusinversustotalisandjuvenilerheumaticcriticalmitralstenosiscasereport AT mishravikas percutaneousmitralvalvotomyinacaseofsitusinversustotalisandjuvenilerheumaticcriticalmitralstenosiscasereport AT varmachandramohan percutaneousmitralvalvotomyinacaseofsitusinversustotalisandjuvenilerheumaticcriticalmitralstenosiscasereport |