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Acute cholangitis in an old patient with Crigler-Najjar syndrome type II - a case report

BACKGROUND: Crigler-Najjar syndrome (CN) is a very rare genetic disorder characterized by an inability to conjugate bilirubin. Contrary to CN type I, patients with CN II exhibit residual capacity to conjugate bilirubin and may present a normal life expectancy. CASE PRESENTATION: We report an unusual...

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Detalles Bibliográficos
Autores principales:	Fernandes, Samuel Raimundo, Moura, Carlos Miguel, Rodrigues, Beatriz, Correia, Luís Araújo, Cortez-Pinto, Helena, Velosa, José
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2016
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4788912/ https://www.ncbi.nlm.nih.gov/pubmed/26968162 http://dx.doi.org/10.1186/s12876-016-0449-9

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