Tracheobronchomegaly as a Cause of Bronchiectasis in an Adult

Mounier-Kuhn syndrome (MKS) is a rare congenital anomaly characterized by dilated trachea and main bronchi due to atrophy of the elastic fibers and smooth muscle cells of the trachea and major airways. Patients of MKS can have varied presentation. The diagnosis is established radiologically and bron...

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Detalles Bibliográficos
Autores principales: Govindaraj, Vishnukanth, Mohanty Mohapatra, Madhusmita, Nagamalli Kumar, Balla, Narayanasami, Suryakala
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2016
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4789050/
https://www.ncbi.nlm.nih.gov/pubmed/27022496
http://dx.doi.org/10.1155/2016/5049406
Descripción
Sumario:Mounier-Kuhn syndrome (MKS) is a rare congenital anomaly characterized by dilated trachea and main bronchi due to atrophy of the elastic fibers and smooth muscle cells of the trachea and major airways. Patients of MKS can have varied presentation. The diagnosis is established radiologically and bronchoscopically. There is no specific treatment for MKS. We present an adult man with MKS who presented with recurrent respiratory tract infection. The diagnosis was confirmed by imaging study and fiberoptic bronchoscopy.

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