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Protein and calorie intakes in adult and pediatric subjects with urea cycle disorders participating in clinical trials of glycerol phenylbutyrate()
BACKGROUND: Little prospectively collected data are available comparing the dietary intake of urea cycle disorder (UCD) patients to UCD treatment guidelines or to healthy individuals. OBJECTIVE: To examine the protein and calorie intakes of UCD subjects who participated in clinical trials of glycero...
Autores principales: | Hook, Debra, Diaz, George A., Lee, Brendan, Bartley, James, Longo, Nicola, Berquist, William, Le Mons, Cynthia, Rudolph-Angelich, Ingrid, Porter, Marty, Scharschmidt, Bruce F., Mokhtarani, Masoud |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4789342/ https://www.ncbi.nlm.nih.gov/pubmed/27014577 http://dx.doi.org/10.1016/j.ymgmr.2015.11.002 |
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