Synovial sarcoma of kidney in a child: A rare presentation

There are no reported cases in the literature of primary renal synovial sarcoma in pediatric patients. The management of renal synovial sarcoma has been extrapolated from the management of soft tissue sarcomas at other sites. We present a 4-year-old female who was suspected to have Wilms’ tumor. The...

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Autores principales: Radhakrishnan, Venkatraman, Dhanushkodi, Manikandan, Narayanswamy, Kathiresan, Raja, Anand, Sundersingh, Shirley, Sagar, Tenali
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2016
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4790133/
https://www.ncbi.nlm.nih.gov/pubmed/27046979
http://dx.doi.org/10.4103/0971-9261.172502
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author Radhakrishnan, Venkatraman
Dhanushkodi, Manikandan
Narayanswamy, Kathiresan
Raja, Anand
Sundersingh, Shirley
Sagar, Tenali
author_facet Radhakrishnan, Venkatraman
Dhanushkodi, Manikandan
Narayanswamy, Kathiresan
Raja, Anand
Sundersingh, Shirley
Sagar, Tenali
author_sort Radhakrishnan, Venkatraman
collection PubMed
description There are no reported cases in the literature of primary renal synovial sarcoma in pediatric patients. The management of renal synovial sarcoma has been extrapolated from the management of soft tissue sarcomas at other sites. We present a 4-year-old female who was suspected to have Wilms’ tumor. The patient underwent guided biopsy as she did not respond to neoadjuvant chemotherapy for Wilms’ tumor. The biopsy was consistent with primary renal synovial sarcoma. The child was treated with change in her neoadjuvant chemotherapy regimen and surgery. The diagnosis of synovial sarcoma was confirmed by demonstrating the t (X, 18) translocation using polymerase chain reaction.
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spelling pubmed-47901332016-04-04 Synovial sarcoma of kidney in a child: A rare presentation Radhakrishnan, Venkatraman Dhanushkodi, Manikandan Narayanswamy, Kathiresan Raja, Anand Sundersingh, Shirley Sagar, Tenali J Indian Assoc Pediatr Surg Case Report There are no reported cases in the literature of primary renal synovial sarcoma in pediatric patients. The management of renal synovial sarcoma has been extrapolated from the management of soft tissue sarcomas at other sites. We present a 4-year-old female who was suspected to have Wilms’ tumor. The patient underwent guided biopsy as she did not respond to neoadjuvant chemotherapy for Wilms’ tumor. The biopsy was consistent with primary renal synovial sarcoma. The child was treated with change in her neoadjuvant chemotherapy regimen and surgery. The diagnosis of synovial sarcoma was confirmed by demonstrating the t (X, 18) translocation using polymerase chain reaction. Medknow Publications & Media Pvt Ltd 2016 /pmc/articles/PMC4790133/ /pubmed/27046979 http://dx.doi.org/10.4103/0971-9261.172502 Text en Copyright: © Journal of Indian Association of Pediatric Surgeons http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Case Report
Radhakrishnan, Venkatraman
Dhanushkodi, Manikandan
Narayanswamy, Kathiresan
Raja, Anand
Sundersingh, Shirley
Sagar, Tenali
Synovial sarcoma of kidney in a child: A rare presentation
title Synovial sarcoma of kidney in a child: A rare presentation
title_full Synovial sarcoma of kidney in a child: A rare presentation
title_fullStr Synovial sarcoma of kidney in a child: A rare presentation
title_full_unstemmed Synovial sarcoma of kidney in a child: A rare presentation
title_short Synovial sarcoma of kidney in a child: A rare presentation
title_sort synovial sarcoma of kidney in a child: a rare presentation
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4790133/
https://www.ncbi.nlm.nih.gov/pubmed/27046979
http://dx.doi.org/10.4103/0971-9261.172502
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