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Combined defects in oxidative phosphorylation and fatty acid β-oxidation in mitochondrial disease

Mitochondria provide the main source of energy to eukaryotic cells, oxidizing fats and sugars to generate ATP. Mitochondrial fatty acid β-oxidation (FAO) and oxidative phosphorylation (OXPHOS) are two metabolic pathways which are central to this process. Defects in these pathways can result in disea...

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Detalles Bibliográficos
Autores principales:	Nsiah-Sefaa, Abena, McKenzie, Matthew
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Portland Press Ltd. 2016
Materias:	Review Articles
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4793296/ https://www.ncbi.nlm.nih.gov/pubmed/26839416 http://dx.doi.org/10.1042/BSR20150295

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