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Brain Lipotoxicity of Phytanic Acid and Very Long-chain Fatty Acids. Harmful Cellular/Mitochondrial Activities in Refsum Disease and X-Linked Adrenoleukodystrophy

It is increasingly understood that in the aging brain, especially in the case of patients suffering from neurodegenerative diseases, some fatty acids at pathologically high concentrations exert detrimental activities. To study such activities, we here analyze genetic diseases, which are due to compr...

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Detalles Bibliográficos
Autores principales:	Schönfeld, Peter, Reiser, Georg
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	JKL International LLC 2016
Materias:	Review Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4809606/ https://www.ncbi.nlm.nih.gov/pubmed/27114847 http://dx.doi.org/10.14336/AD.2015.0823

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