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Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult

Intimomedial mucoid degeneration (IMMD) is characterised by aneurysm formation following mucin deposition in the intima and media, with elastic tissue degeneration of the arterial wall. We present a case of a young adult who developed a diffusely aneurysmal aorta and its major branches, which was hi...

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Autores principales: Viljoen, Charle, Szymanksi, Patryk, Osman, Naeem, Henning, Kristin Lorenc, ScholtZ, Paul, Rayner, Brian, Naidoo, Nadraj
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Clinics Cardive Publishing 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4817203/
https://www.ncbi.nlm.nih.gov/pubmed/26956498
http://dx.doi.org/10.5830/CVJA-2015-079
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author Viljoen, Charle
Szymanksi, Patryk
Osman, Naeem
Henning, Kristin Lorenc
ScholtZ, Paul
Rayner, Brian
Naidoo, Nadraj
author_facet Viljoen, Charle
Szymanksi, Patryk
Osman, Naeem
Henning, Kristin Lorenc
ScholtZ, Paul
Rayner, Brian
Naidoo, Nadraj
author_sort Viljoen, Charle
collection PubMed
description Intimomedial mucoid degeneration (IMMD) is characterised by aneurysm formation following mucin deposition in the intima and media, with elastic tissue degeneration of the arterial wall. We present a case of a young adult who developed a diffusely aneurysmal aorta and its major branches, which was histopathologically confirmed as intimomedial mucoid degeneration, and a review of the literature. This case report attempts to raise the awareness of the reader to this rare cause of aortic aneurysm and to the bleeding diathesis associated with IMMD that may complicate surgery.
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spelling pubmed-48172032016-04-22 Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult Viljoen, Charle Szymanksi, Patryk Osman, Naeem Henning, Kristin Lorenc ScholtZ, Paul Rayner, Brian Naidoo, Nadraj Cardiovasc J Afr Cardiovascular Topics Intimomedial mucoid degeneration (IMMD) is characterised by aneurysm formation following mucin deposition in the intima and media, with elastic tissue degeneration of the arterial wall. We present a case of a young adult who developed a diffusely aneurysmal aorta and its major branches, which was histopathologically confirmed as intimomedial mucoid degeneration, and a review of the literature. This case report attempts to raise the awareness of the reader to this rare cause of aortic aneurysm and to the bleeding diathesis associated with IMMD that may complicate surgery. Clinics Cardive Publishing 2016 /pmc/articles/PMC4817203/ /pubmed/26956498 http://dx.doi.org/10.5830/CVJA-2015-079 Text en Copyright © 2015 Clinics Cardive Publishing http://creativecommons.org/licenses/by/2.5/ This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Cardiovascular Topics
Viljoen, Charle
Szymanksi, Patryk
Osman, Naeem
Henning, Kristin Lorenc
ScholtZ, Paul
Rayner, Brian
Naidoo, Nadraj
Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult
title Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult
title_full Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult
title_fullStr Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult
title_full_unstemmed Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult
title_short Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult
title_sort intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult
topic Cardiovascular Topics
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4817203/
https://www.ncbi.nlm.nih.gov/pubmed/26956498
http://dx.doi.org/10.5830/CVJA-2015-079
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