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Hyaline fibromatosis syndrome: cutaneous manifestations

Hyaline fibromatosis syndrome is the current name for clinical manifestations of diseases previously known as “infantile systemic hyalinosis” and “juvenile hyaline fibromatosis”. The authors report representative clinical cases of each one of the above subtypes with emphasis on cutaneous manifestati...

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Autores principales: Marques, Silvio Alencar, Stolf, Hamilton Ometto, Polizel, Juliana Ocanha, Munhoz, Tânia, Brandão, Marcela Calixto, Marques, Mariangela Esther Alencar
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Dermatologia 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4861574/
https://www.ncbi.nlm.nih.gov/pubmed/27192526
http://dx.doi.org/10.1590/abd1806-4841.20163799
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author Marques, Silvio Alencar
Stolf, Hamilton Ometto
Polizel, Juliana Ocanha
Munhoz, Tânia
Brandão, Marcela Calixto
Marques, Mariangela Esther Alencar
author_facet Marques, Silvio Alencar
Stolf, Hamilton Ometto
Polizel, Juliana Ocanha
Munhoz, Tânia
Brandão, Marcela Calixto
Marques, Mariangela Esther Alencar
author_sort Marques, Silvio Alencar
collection PubMed
description Hyaline fibromatosis syndrome is the current name for clinical manifestations of diseases previously known as “infantile systemic hyalinosis” and “juvenile hyaline fibromatosis”. The authors report representative clinical cases of each one of the above subtypes with emphasis on cutaneous manifestations and difficulties for early diagnosis in this syndrome, essentially of multidisciplinary approach.
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spelling pubmed-48615742016-05-10 Hyaline fibromatosis syndrome: cutaneous manifestations Marques, Silvio Alencar Stolf, Hamilton Ometto Polizel, Juliana Ocanha Munhoz, Tânia Brandão, Marcela Calixto Marques, Mariangela Esther Alencar An Bras Dermatol Case Report Hyaline fibromatosis syndrome is the current name for clinical manifestations of diseases previously known as “infantile systemic hyalinosis” and “juvenile hyaline fibromatosis”. The authors report representative clinical cases of each one of the above subtypes with emphasis on cutaneous manifestations and difficulties for early diagnosis in this syndrome, essentially of multidisciplinary approach. Sociedade Brasileira de Dermatologia 2016 /pmc/articles/PMC4861574/ /pubmed/27192526 http://dx.doi.org/10.1590/abd1806-4841.20163799 Text en © 2016 by Anais Brasileiros de Dermatologia http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License which permits unrestricted non-commercial use, distribution, and reproduction in any medium provided the original work is properly cited.
spellingShingle Case Report
Marques, Silvio Alencar
Stolf, Hamilton Ometto
Polizel, Juliana Ocanha
Munhoz, Tânia
Brandão, Marcela Calixto
Marques, Mariangela Esther Alencar
Hyaline fibromatosis syndrome: cutaneous manifestations
title Hyaline fibromatosis syndrome: cutaneous manifestations
title_full Hyaline fibromatosis syndrome: cutaneous manifestations
title_fullStr Hyaline fibromatosis syndrome: cutaneous manifestations
title_full_unstemmed Hyaline fibromatosis syndrome: cutaneous manifestations
title_short Hyaline fibromatosis syndrome: cutaneous manifestations
title_sort hyaline fibromatosis syndrome: cutaneous manifestations
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4861574/
https://www.ncbi.nlm.nih.gov/pubmed/27192526
http://dx.doi.org/10.1590/abd1806-4841.20163799
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