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Pelvic alveolar rhabdomyosarcoma in a young adult
Rhabdomyosarcomas are soft-tissue tumors, rare in adults. Accounting for nearly 5% of childhood cancers, they represent less than 0.03% of adult malignancies (1, 2). Three different subtypes of rhabdomyosarcoma have been described (embryonal, alveolar and pleomorphic), making up approximately 50%, 3...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2015
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4861885/ https://www.ncbi.nlm.nih.gov/pubmed/27190552 http://dx.doi.org/10.2484/rcr.v9i4.798 |
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author | Reisner, David Amadi, Chiemezie Beckman, Irwin Patel, Shweta Surampudi, Ramana |
author_facet | Reisner, David Amadi, Chiemezie Beckman, Irwin Patel, Shweta Surampudi, Ramana |
author_sort | Reisner, David |
collection | PubMed |
description | Rhabdomyosarcomas are soft-tissue tumors, rare in adults. Accounting for nearly 5% of childhood cancers, they represent less than 0.03% of adult malignancies (1, 2). Three different subtypes of rhabdomyosarcoma have been described (embryonal, alveolar and pleomorphic), making up approximately 50%, 30%, and 20% of the cases, respectively (3). Although the definitive diagnosis is made pathologically, some distinguishing features among these subtypes, and between rhabdomyosarcomas and other soft-tissue tumors, can be suggested on MRI and CT. We present an interesting case of a 20-year-old female with a locally aggressive pelvic alveolar rhabdomyosarcoma. While the prognosis has improved with newer treatment techniques, overall survival rates remain poor. Our case study presents typical features of a rare disease, which can often present a diagnostic dilemma for clinicians. |
format | Online Article Text |
id | pubmed-4861885 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2015 |
publisher | Elsevier |
record_format | MEDLINE/PubMed |
spelling | pubmed-48618852016-05-17 Pelvic alveolar rhabdomyosarcoma in a young adult Reisner, David Amadi, Chiemezie Beckman, Irwin Patel, Shweta Surampudi, Ramana Radiol Case Rep Article Rhabdomyosarcomas are soft-tissue tumors, rare in adults. Accounting for nearly 5% of childhood cancers, they represent less than 0.03% of adult malignancies (1, 2). Three different subtypes of rhabdomyosarcoma have been described (embryonal, alveolar and pleomorphic), making up approximately 50%, 30%, and 20% of the cases, respectively (3). Although the definitive diagnosis is made pathologically, some distinguishing features among these subtypes, and between rhabdomyosarcomas and other soft-tissue tumors, can be suggested on MRI and CT. We present an interesting case of a 20-year-old female with a locally aggressive pelvic alveolar rhabdomyosarcoma. While the prognosis has improved with newer treatment techniques, overall survival rates remain poor. Our case study presents typical features of a rare disease, which can often present a diagnostic dilemma for clinicians. Elsevier 2015-11-06 /pmc/articles/PMC4861885/ /pubmed/27190552 http://dx.doi.org/10.2484/rcr.v9i4.798 Text en © 2014 The Authors. http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Article Reisner, David Amadi, Chiemezie Beckman, Irwin Patel, Shweta Surampudi, Ramana Pelvic alveolar rhabdomyosarcoma in a young adult |
title | Pelvic alveolar rhabdomyosarcoma in a young adult |
title_full | Pelvic alveolar rhabdomyosarcoma in a young adult |
title_fullStr | Pelvic alveolar rhabdomyosarcoma in a young adult |
title_full_unstemmed | Pelvic alveolar rhabdomyosarcoma in a young adult |
title_short | Pelvic alveolar rhabdomyosarcoma in a young adult |
title_sort | pelvic alveolar rhabdomyosarcoma in a young adult |
topic | Article |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4861885/ https://www.ncbi.nlm.nih.gov/pubmed/27190552 http://dx.doi.org/10.2484/rcr.v9i4.798 |
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