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Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor

Dermatofibrosarcoma protuberans (DFSP) is a rare soft tumor which originally represents a cutaneous sarcoma. It grows slowly and presents usually as nodular superficial lesion on the trunk or the extremities. Although these tumors are locally aggressive with high rate of recurrence following surgery...

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Autores principales: Al Barwani, Aliya Sarhan, Taif, Sawsan, Al Mazrouai, Reem Ahmed, Al Muzahmi, Khamis Salim, Alrawi, Asif
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4863404/
https://www.ncbi.nlm.nih.gov/pubmed/27195182
http://dx.doi.org/10.4103/2156-7514.181492
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author Al Barwani, Aliya Sarhan
Taif, Sawsan
Al Mazrouai, Reem Ahmed
Al Muzahmi, Khamis Salim
Alrawi, Asif
author_facet Al Barwani, Aliya Sarhan
Taif, Sawsan
Al Mazrouai, Reem Ahmed
Al Muzahmi, Khamis Salim
Alrawi, Asif
author_sort Al Barwani, Aliya Sarhan
collection PubMed
description Dermatofibrosarcoma protuberans (DFSP) is a rare soft tumor which originally represents a cutaneous sarcoma. It grows slowly and presents usually as nodular superficial lesion on the trunk or the extremities. Although these tumors are locally aggressive with high rate of recurrence following surgery; the prognosis is considered excellent when it is effectively treated. The radiological appearance of this tumor has rarely been studied and findings infrequently discussed in the literature probably because many lesions underwent resection before imaging. Although imaging is infrequently performed for this lesion; it can show characteristic features and demonstrate the full extent. Imaging may also play a role in the differentiation of this tumor from more serious soft tissue lesions such as more aggressive sarcomas and hemangioma. In this article, we discuss the imaging findings of DFSP that can aid in its diagnosis and its variable appearances. In addition; the clinical presentation and treatment options are also described with review of the previous literature.
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spelling pubmed-48634042016-05-18 Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor Al Barwani, Aliya Sarhan Taif, Sawsan Al Mazrouai, Reem Ahmed Al Muzahmi, Khamis Salim Alrawi, Asif J Clin Imaging Sci Review Article Dermatofibrosarcoma protuberans (DFSP) is a rare soft tumor which originally represents a cutaneous sarcoma. It grows slowly and presents usually as nodular superficial lesion on the trunk or the extremities. Although these tumors are locally aggressive with high rate of recurrence following surgery; the prognosis is considered excellent when it is effectively treated. The radiological appearance of this tumor has rarely been studied and findings infrequently discussed in the literature probably because many lesions underwent resection before imaging. Although imaging is infrequently performed for this lesion; it can show characteristic features and demonstrate the full extent. Imaging may also play a role in the differentiation of this tumor from more serious soft tissue lesions such as more aggressive sarcomas and hemangioma. In this article, we discuss the imaging findings of DFSP that can aid in its diagnosis and its variable appearances. In addition; the clinical presentation and treatment options are also described with review of the previous literature. Medknow Publications & Media Pvt Ltd 2016-04-29 /pmc/articles/PMC4863404/ /pubmed/27195182 http://dx.doi.org/10.4103/2156-7514.181492 Text en Copyright: © 2016 Journal of Clinical Imaging Science http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Review Article
Al Barwani, Aliya Sarhan
Taif, Sawsan
Al Mazrouai, Reem Ahmed
Al Muzahmi, Khamis Salim
Alrawi, Asif
Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor
title Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor
title_full Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor
title_fullStr Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor
title_full_unstemmed Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor
title_short Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor
title_sort dermatofibrosarcoma protuberans: insights into a rare soft tissue tumor
topic Review Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4863404/
https://www.ncbi.nlm.nih.gov/pubmed/27195182
http://dx.doi.org/10.4103/2156-7514.181492
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