A case of pancreatitis, panniculitis and polyarthritis syndrome: Elucidating the pathophysiologic mechanisms of a rare condition

Pancreatitis-Panniculitis-Polyarthritis (PPP) syndrome is rare and its physiopathology unclear. A 6-year old boy suffered of traumatic pancreatitis complicated by PPP syndrome. Extensive investigations demonstrated high levels of pancreatic lipase and fatty acids in the affected peripheral tissues....

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Autores principales: Loverdos, Ines, Swan, Marc C., Shekherdimian, Shant, Al-Rasheed, Abdulrahman A., Schneider, Rayfel, Fish, Joel S., Ngan, Bo-Yee, Adeli, Khosrow, Lowe, Mark E., Singh, Vijay P., Sevilla, Wednesday Marie A., Langer, Jacob C., Gonska, Tanja
Formato: Online Artículo Texto
Lenguaje:English
Publicado: 2015
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4864014/
https://www.ncbi.nlm.nih.gov/pubmed/27182490
http://dx.doi.org/10.1016/j.epsc.2015.03.014
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author Loverdos, Ines
Swan, Marc C.
Shekherdimian, Shant
Al-Rasheed, Abdulrahman A.
Schneider, Rayfel
Fish, Joel S.
Ngan, Bo-Yee
Adeli, Khosrow
Lowe, Mark E.
Singh, Vijay P.
Sevilla, Wednesday Marie A.
Langer, Jacob C.
Gonska, Tanja
author_facet Loverdos, Ines
Swan, Marc C.
Shekherdimian, Shant
Al-Rasheed, Abdulrahman A.
Schneider, Rayfel
Fish, Joel S.
Ngan, Bo-Yee
Adeli, Khosrow
Lowe, Mark E.
Singh, Vijay P.
Sevilla, Wednesday Marie A.
Langer, Jacob C.
Gonska, Tanja
author_sort Loverdos, Ines
collection PubMed
description Pancreatitis-Panniculitis-Polyarthritis (PPP) syndrome is rare and its physiopathology unclear. A 6-year old boy suffered of traumatic pancreatitis complicated by PPP syndrome. Extensive investigations demonstrated high levels of pancreatic lipase and fatty acids in the affected peripheral tissues. These findings support the sequence of peripheral lipolysis and fatty acid accumulation inducing tissue inflammation.
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spelling pubmed-48640142016-05-12 A case of pancreatitis, panniculitis and polyarthritis syndrome: Elucidating the pathophysiologic mechanisms of a rare condition Loverdos, Ines Swan, Marc C. Shekherdimian, Shant Al-Rasheed, Abdulrahman A. Schneider, Rayfel Fish, Joel S. Ngan, Bo-Yee Adeli, Khosrow Lowe, Mark E. Singh, Vijay P. Sevilla, Wednesday Marie A. Langer, Jacob C. Gonska, Tanja J Pediatr Surg Case Rep Article Pancreatitis-Panniculitis-Polyarthritis (PPP) syndrome is rare and its physiopathology unclear. A 6-year old boy suffered of traumatic pancreatitis complicated by PPP syndrome. Extensive investigations demonstrated high levels of pancreatic lipase and fatty acids in the affected peripheral tissues. These findings support the sequence of peripheral lipolysis and fatty acid accumulation inducing tissue inflammation. 2015-05 /pmc/articles/PMC4864014/ /pubmed/27182490 http://dx.doi.org/10.1016/j.epsc.2015.03.014 Text en http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Article
Loverdos, Ines
Swan, Marc C.
Shekherdimian, Shant
Al-Rasheed, Abdulrahman A.
Schneider, Rayfel
Fish, Joel S.
Ngan, Bo-Yee
Adeli, Khosrow
Lowe, Mark E.
Singh, Vijay P.
Sevilla, Wednesday Marie A.
Langer, Jacob C.
Gonska, Tanja
A case of pancreatitis, panniculitis and polyarthritis syndrome: Elucidating the pathophysiologic mechanisms of a rare condition
title A case of pancreatitis, panniculitis and polyarthritis syndrome: Elucidating the pathophysiologic mechanisms of a rare condition
title_full A case of pancreatitis, panniculitis and polyarthritis syndrome: Elucidating the pathophysiologic mechanisms of a rare condition
title_fullStr A case of pancreatitis, panniculitis and polyarthritis syndrome: Elucidating the pathophysiologic mechanisms of a rare condition
title_full_unstemmed A case of pancreatitis, panniculitis and polyarthritis syndrome: Elucidating the pathophysiologic mechanisms of a rare condition
title_short A case of pancreatitis, panniculitis and polyarthritis syndrome: Elucidating the pathophysiologic mechanisms of a rare condition
title_sort case of pancreatitis, panniculitis and polyarthritis syndrome: elucidating the pathophysiologic mechanisms of a rare condition
topic Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4864014/
https://www.ncbi.nlm.nih.gov/pubmed/27182490
http://dx.doi.org/10.1016/j.epsc.2015.03.014
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