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Muscle wasting and adipose tissue browning in infantile nephropathic cystinosis

BACKGROUND: Muscle wasting is a common complication in patients with infantile nephropathic cystinosis, but its mechanism and association with energy metabolism is not known. We define the metabolic phenotype in Ctns(−/−) mice, an established murine model of infantile nephropathic cystinosis, with f...

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Detalles Bibliográficos
Autores principales:	Cheung, Wai W., Cherqui, Stephanie, Ding, Wei, Esparza, Mary, Zhou, Ping, Shao, Jianhua, Lieber, Richard L., Mak, Robert H.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley and Sons Inc. 2015
Materias:	Original Articles
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4864942/ https://www.ncbi.nlm.nih.gov/pubmed/27493869 http://dx.doi.org/10.1002/jcsm.12056

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