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Inflammatory myofibroblastic tumor presenting as ileocecal intussusception—A case report

INTRODUCTION: Inflammatory myofibroblastic tumor (IMFT) is an uncommon mesenchymal solid tumor commonly documented in children and young adults. It is usually located in lungs however, extrapulmonary involvement has also been reported. Here we report a case of IMFT presenting as an ileocecal intussu...

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Autores principales: Paiva, Cláudia, Soares, Filomena, da Inez Correia, Raquel, Valente, Vítor
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4900436/
https://www.ncbi.nlm.nih.gov/pubmed/27262346
http://dx.doi.org/10.1016/j.ijscr.2016.05.027
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author Paiva, Cláudia
Soares, Filomena
da Inez Correia, Raquel
Valente, Vítor
author_facet Paiva, Cláudia
Soares, Filomena
da Inez Correia, Raquel
Valente, Vítor
author_sort Paiva, Cláudia
collection PubMed
description INTRODUCTION: Inflammatory myofibroblastic tumor (IMFT) is an uncommon mesenchymal solid tumor commonly documented in children and young adults. It is usually located in lungs however, extrapulmonary involvement has also been reported. Here we report a case of IMFT presenting as an ileocecal intussusception. PRESENTATION OF CASE: A 55-year-old man presented with a two months history of colicky abdominal pain, more intense at the right inferior abdominal quadrant, and unintentional weight loss of 8 kg in the previous four months. Computer tomography showed an image of intussusception at the cecum. Colonoscopy demonstrated a pediculated tubular lesion, with the base near ileocecal valve. We performed a right hemicolectomy. Histopathological examination of the tumor revealed an IMFT. DISCUSSION: IMFT usually affects lungs with rare gastrointestinal involvement. Clinical presentation is related with location of the neoplasm. Intussusception in adults presents with non-specific symptoms and classical image signs facilitate preoperative diagnosis. IMFT diagnosis is histopathological which usually implies surgical resection. Complete surgical excision, with microscopically clear margins, is the mainstain of treatment, with virtually no local recurrence or metastasis. CONCLUSION: Gastrointestinal IMFT are rare in the adult population and clinical features depend on its location. Surgical approach with total excision of the neoplasm confirms the diagnosis. Prognosis is good with the main prognostic indicator being the adequacy of the primary excision.
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spelling pubmed-49004362016-06-21 Inflammatory myofibroblastic tumor presenting as ileocecal intussusception—A case report Paiva, Cláudia Soares, Filomena da Inez Correia, Raquel Valente, Vítor Int J Surg Case Rep Case Report INTRODUCTION: Inflammatory myofibroblastic tumor (IMFT) is an uncommon mesenchymal solid tumor commonly documented in children and young adults. It is usually located in lungs however, extrapulmonary involvement has also been reported. Here we report a case of IMFT presenting as an ileocecal intussusception. PRESENTATION OF CASE: A 55-year-old man presented with a two months history of colicky abdominal pain, more intense at the right inferior abdominal quadrant, and unintentional weight loss of 8 kg in the previous four months. Computer tomography showed an image of intussusception at the cecum. Colonoscopy demonstrated a pediculated tubular lesion, with the base near ileocecal valve. We performed a right hemicolectomy. Histopathological examination of the tumor revealed an IMFT. DISCUSSION: IMFT usually affects lungs with rare gastrointestinal involvement. Clinical presentation is related with location of the neoplasm. Intussusception in adults presents with non-specific symptoms and classical image signs facilitate preoperative diagnosis. IMFT diagnosis is histopathological which usually implies surgical resection. Complete surgical excision, with microscopically clear margins, is the mainstain of treatment, with virtually no local recurrence or metastasis. CONCLUSION: Gastrointestinal IMFT are rare in the adult population and clinical features depend on its location. Surgical approach with total excision of the neoplasm confirms the diagnosis. Prognosis is good with the main prognostic indicator being the adequacy of the primary excision. Elsevier 2016-05-19 /pmc/articles/PMC4900436/ /pubmed/27262346 http://dx.doi.org/10.1016/j.ijscr.2016.05.027 Text en © 2016 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Paiva, Cláudia
Soares, Filomena
da Inez Correia, Raquel
Valente, Vítor
Inflammatory myofibroblastic tumor presenting as ileocecal intussusception—A case report
title Inflammatory myofibroblastic tumor presenting as ileocecal intussusception—A case report
title_full Inflammatory myofibroblastic tumor presenting as ileocecal intussusception—A case report
title_fullStr Inflammatory myofibroblastic tumor presenting as ileocecal intussusception—A case report
title_full_unstemmed Inflammatory myofibroblastic tumor presenting as ileocecal intussusception—A case report
title_short Inflammatory myofibroblastic tumor presenting as ileocecal intussusception—A case report
title_sort inflammatory myofibroblastic tumor presenting as ileocecal intussusception—a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4900436/
https://www.ncbi.nlm.nih.gov/pubmed/27262346
http://dx.doi.org/10.1016/j.ijscr.2016.05.027
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