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A rare cause of cystic lung disease – Birt-Hogg-Dubé syndrome
Birt-Hogg-Dubé syndrome, initially described in 1977, is an autosomal dominant inherited condition characterised by basal pulmonary cysts often resulting in pneumothorax, renal tumours and cutaneous involvement. Lung cysts have been described in up to 90% of patients with a corresponding risk of pne...
| Autores principales: | , , |
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| Formato: | Online Artículo Texto |
| Lenguaje: | English |
| Publicado: |
Elsevier
2016
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| Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4900472/ https://www.ncbi.nlm.nih.gov/pubmed/27330962 http://dx.doi.org/10.1016/j.rmcr.2016.05.007 |