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Neurodegeneration and Epilepsy in a Zebrafish Model of CLN3 Disease (Batten Disease)

The neuronal ceroid lipofuscinoses are a group of lysosomal storage disorders that comprise the most common, genetically heterogeneous, fatal neurodegenerative disorders of children. They are characterised by childhood onset, visual failure, epileptic seizures, psychomotor retardation and dementia....

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Detalles Bibliográficos
Autores principales:	Wager, Kim, Zdebik, Anselm A., Fu, Sonia, Cooper, Jonathan D., Harvey, Robert J., Russell, Claire
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2016
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4915684/ https://www.ncbi.nlm.nih.gov/pubmed/27327661 http://dx.doi.org/10.1371/journal.pone.0157365

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