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Multiple pterygium syndrome: Challenge for anesthesiologist
Multiple pterygium syndrome (MPS) is a very rare autosomal recessive disorder characterized by flexion of joint and digit contractures, skin webbing, cleft palate, deformity of the spine, and cervical spine fusion. Difficult airway is associated mainly due to micrognathia, retrognathia, webbing of t...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4916826/ https://www.ncbi.nlm.nih.gov/pubmed/27375397 http://dx.doi.org/10.4103/1658-354X.174901 |
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author | Sethi, P Bhatia, PK Gupta, N Singh, K |
author_facet | Sethi, P Bhatia, PK Gupta, N Singh, K |
author_sort | Sethi, P |
collection | PubMed |
description | Multiple pterygium syndrome (MPS) is a very rare autosomal recessive disorder characterized by flexion of joint and digit contractures, skin webbing, cleft palate, deformity of the spine, and cervical spine fusion. Difficult airway is associated mainly due to micrognathia, retrognathia, webbing of the neck, and limitation of the mouth opening and neck extension. We are reporting a case of a 5-year-old female diagnosed with MPS and exhibiting a bilateral club foot and congenital vertical talus. The patient was posted for manipulation and above the knee casting under general anesthesia. |
format | Online Article Text |
id | pubmed-4916826 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-49168262016-07-02 Multiple pterygium syndrome: Challenge for anesthesiologist Sethi, P Bhatia, PK Gupta, N Singh, K Saudi J Anaesth Case Report Multiple pterygium syndrome (MPS) is a very rare autosomal recessive disorder characterized by flexion of joint and digit contractures, skin webbing, cleft palate, deformity of the spine, and cervical spine fusion. Difficult airway is associated mainly due to micrognathia, retrognathia, webbing of the neck, and limitation of the mouth opening and neck extension. We are reporting a case of a 5-year-old female diagnosed with MPS and exhibiting a bilateral club foot and congenital vertical talus. The patient was posted for manipulation and above the knee casting under general anesthesia. Medknow Publications & Media Pvt Ltd 2016 /pmc/articles/PMC4916826/ /pubmed/27375397 http://dx.doi.org/10.4103/1658-354X.174901 Text en Copyright: © Saudi Journal of Anaesthesia http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution NonCommercial ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non commercially, as long as the author is credited and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Sethi, P Bhatia, PK Gupta, N Singh, K Multiple pterygium syndrome: Challenge for anesthesiologist |
title | Multiple pterygium syndrome: Challenge for anesthesiologist |
title_full | Multiple pterygium syndrome: Challenge for anesthesiologist |
title_fullStr | Multiple pterygium syndrome: Challenge for anesthesiologist |
title_full_unstemmed | Multiple pterygium syndrome: Challenge for anesthesiologist |
title_short | Multiple pterygium syndrome: Challenge for anesthesiologist |
title_sort | multiple pterygium syndrome: challenge for anesthesiologist |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4916826/ https://www.ncbi.nlm.nih.gov/pubmed/27375397 http://dx.doi.org/10.4103/1658-354X.174901 |
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