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A rare cause of recurrent aortic dissection
We report the case of a 19-year-old man with a history of Loeys–Dietz syndrome (LDS), which was diagnosed when he had a Stanford type A aortic dissection. He also had multiple aneurysms including ones in the innominate, right common carotid, and right internal mammary arteries. He had had multiple p...
Autores principales: | , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4917711/ https://www.ncbi.nlm.nih.gov/pubmed/27358537 http://dx.doi.org/10.1016/j.jsha.2015.11.005 |
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author | Agrawal, Yashwant Gupta, Vishal |
author_facet | Agrawal, Yashwant Gupta, Vishal |
author_sort | Agrawal, Yashwant |
collection | PubMed |
description | We report the case of a 19-year-old man with a history of Loeys–Dietz syndrome (LDS), which was diagnosed when he had a Stanford type A aortic dissection. He also had multiple aneurysms including ones in the innominate, right common carotid, and right internal mammary arteries. He had had multiple procedures including Bentall’s procedure, repeat sternotomy with complete arch and valve replacement, and coil embolization of internal mammary artery aneurysm in the past. His LDS was characterized by gene mutation for transforming growth factor-β receptor 1. He presented to our facility with sudden onset of back pain, radiating to the right shoulder and chest. He was diagnosed with Stanford type B aortic dissection and underwent thoracic aorta endovascular repair for his aortic dissection. This case represents the broad spectrum of pathology associated with LDS where even with regular surveillance and aggressive medical management the patient developed Stanford B aortic dissection. |
format | Online Article Text |
id | pubmed-4917711 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Elsevier |
record_format | MEDLINE/PubMed |
spelling | pubmed-49177112016-06-29 A rare cause of recurrent aortic dissection Agrawal, Yashwant Gupta, Vishal J Saudi Heart Assoc Case Report We report the case of a 19-year-old man with a history of Loeys–Dietz syndrome (LDS), which was diagnosed when he had a Stanford type A aortic dissection. He also had multiple aneurysms including ones in the innominate, right common carotid, and right internal mammary arteries. He had had multiple procedures including Bentall’s procedure, repeat sternotomy with complete arch and valve replacement, and coil embolization of internal mammary artery aneurysm in the past. His LDS was characterized by gene mutation for transforming growth factor-β receptor 1. He presented to our facility with sudden onset of back pain, radiating to the right shoulder and chest. He was diagnosed with Stanford type B aortic dissection and underwent thoracic aorta endovascular repair for his aortic dissection. This case represents the broad spectrum of pathology associated with LDS where even with regular surveillance and aggressive medical management the patient developed Stanford B aortic dissection. Elsevier 2016-07 2015-11-21 /pmc/articles/PMC4917711/ /pubmed/27358537 http://dx.doi.org/10.1016/j.jsha.2015.11.005 Text en © 2015 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Case Report Agrawal, Yashwant Gupta, Vishal A rare cause of recurrent aortic dissection |
title | A rare cause of recurrent aortic dissection |
title_full | A rare cause of recurrent aortic dissection |
title_fullStr | A rare cause of recurrent aortic dissection |
title_full_unstemmed | A rare cause of recurrent aortic dissection |
title_short | A rare cause of recurrent aortic dissection |
title_sort | rare cause of recurrent aortic dissection |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4917711/ https://www.ncbi.nlm.nih.gov/pubmed/27358537 http://dx.doi.org/10.1016/j.jsha.2015.11.005 |
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