Congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma

INTRODUCTION: Afibrinogenemia is a rare coagulation disorder. Clinical features of spontaneous bleeding, bleeding after minor trauma, or after surgery have been described as well as thrombo-embolic complications. In this article, we presented the case of a 19-year old female with congenital afibrino...

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Autores principales: Malaquin, Stephanie, Rebibo, Lionel, Chivot, Cyril, Badoux, Louise, Mahjoub, Yazine, Dupont, Herve
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer Health 2016
Materias:
3900
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4956798/
https://www.ncbi.nlm.nih.gov/pubmed/27428204
http://dx.doi.org/10.1097/MD.0000000000004150
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author Malaquin, Stephanie
Rebibo, Lionel
Chivot, Cyril
Badoux, Louise
Mahjoub, Yazine
Dupont, Herve
author_facet Malaquin, Stephanie
Rebibo, Lionel
Chivot, Cyril
Badoux, Louise
Mahjoub, Yazine
Dupont, Herve
author_sort Malaquin, Stephanie
collection PubMed
description INTRODUCTION: Afibrinogenemia is a rare coagulation disorder. Clinical features of spontaneous bleeding, bleeding after minor trauma, or after surgery have been described as well as thrombo-embolic complications. In this article, we presented the case of a 19-year old female with congenital afibrinogenemia who was admitted with a spontaneous intrahepatic hematoma. CONCLUSIONS: Supportive treatment including transfusion and fibrinogen administration, associated with repeated packing surgeries and selective embolization, were successfully performed.
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spelling pubmed-49567982016-08-02 Congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma Malaquin, Stephanie Rebibo, Lionel Chivot, Cyril Badoux, Louise Mahjoub, Yazine Dupont, Herve Medicine (Baltimore) 3900 INTRODUCTION: Afibrinogenemia is a rare coagulation disorder. Clinical features of spontaneous bleeding, bleeding after minor trauma, or after surgery have been described as well as thrombo-embolic complications. In this article, we presented the case of a 19-year old female with congenital afibrinogenemia who was admitted with a spontaneous intrahepatic hematoma. CONCLUSIONS: Supportive treatment including transfusion and fibrinogen administration, associated with repeated packing surgeries and selective embolization, were successfully performed. Wolters Kluwer Health 2016-07-18 /pmc/articles/PMC4956798/ /pubmed/27428204 http://dx.doi.org/10.1097/MD.0000000000004150 Text en Copyright © 2016 the Author(s). Published by Wolters Kluwer Health, Inc. All rights reserved. http://creativecommons.org/licenses/by/4.0 This is an open access article distributed under the Creative Commons Attribution License 4.0, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. http://creativecommons.org/licenses/by/4.0
spellingShingle 3900
Malaquin, Stephanie
Rebibo, Lionel
Chivot, Cyril
Badoux, Louise
Mahjoub, Yazine
Dupont, Herve
Congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma
title Congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma
title_full Congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma
title_fullStr Congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma
title_full_unstemmed Congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma
title_short Congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma
title_sort congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma
topic 3900
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4956798/
https://www.ncbi.nlm.nih.gov/pubmed/27428204
http://dx.doi.org/10.1097/MD.0000000000004150
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