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Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach

Adrenocortical carcinoma is a rare malignancy. Due to late diagnosis and no adequate effective adjuvant treatment, prognosis remains poor. Only approximately 30% of these malignancies are confined to the adrenal gland when they are diagnosed, as these tumors tend to be found years after their genesi...

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Detalles Bibliográficos
Autores principales: Iezzi, Federica, Quarti, Andrea, Surace, Chiara, Pozzi, Marco
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4963988/
https://www.ncbi.nlm.nih.gov/pubmed/27493811
http://dx.doi.org/10.1155/2016/2321017
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author Iezzi, Federica
Quarti, Andrea
Surace, Chiara
Pozzi, Marco
author_facet Iezzi, Federica
Quarti, Andrea
Surace, Chiara
Pozzi, Marco
author_sort Iezzi, Federica
collection PubMed
description Adrenocortical carcinoma is a rare malignancy. Due to late diagnosis and no adequate effective adjuvant treatment, prognosis remains poor. Only approximately 30% of these malignancies are confined to the adrenal gland when they are diagnosed, as these tumors tend to be found years after their genesis. Cardiac involvement of adrenal carcinoma is very rare. We report a rare case of a 7-year-old female with right adrenal cortical carcinoma, involving the right-side heart.
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spelling pubmed-49639882016-08-04 Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach Iezzi, Federica Quarti, Andrea Surace, Chiara Pozzi, Marco Case Rep Cardiol Case Report Adrenocortical carcinoma is a rare malignancy. Due to late diagnosis and no adequate effective adjuvant treatment, prognosis remains poor. Only approximately 30% of these malignancies are confined to the adrenal gland when they are diagnosed, as these tumors tend to be found years after their genesis. Cardiac involvement of adrenal carcinoma is very rare. We report a rare case of a 7-year-old female with right adrenal cortical carcinoma, involving the right-side heart. Hindawi Publishing Corporation 2016 2016-07-14 /pmc/articles/PMC4963988/ /pubmed/27493811 http://dx.doi.org/10.1155/2016/2321017 Text en Copyright © 2016 Federica Iezzi et al. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Iezzi, Federica
Quarti, Andrea
Surace, Chiara
Pozzi, Marco
Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach
title Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach
title_full Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach
title_fullStr Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach
title_full_unstemmed Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach
title_short Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach
title_sort paediatric nonfunctioning adrenocortical carcinoma with extension up to right-side heart: cardiac surgery approach
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4963988/
https://www.ncbi.nlm.nih.gov/pubmed/27493811
http://dx.doi.org/10.1155/2016/2321017
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