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Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach
Adrenocortical carcinoma is a rare malignancy. Due to late diagnosis and no adequate effective adjuvant treatment, prognosis remains poor. Only approximately 30% of these malignancies are confined to the adrenal gland when they are diagnosed, as these tumors tend to be found years after their genesi...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Hindawi Publishing Corporation
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4963988/ https://www.ncbi.nlm.nih.gov/pubmed/27493811 http://dx.doi.org/10.1155/2016/2321017 |
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author | Iezzi, Federica Quarti, Andrea Surace, Chiara Pozzi, Marco |
author_facet | Iezzi, Federica Quarti, Andrea Surace, Chiara Pozzi, Marco |
author_sort | Iezzi, Federica |
collection | PubMed |
description | Adrenocortical carcinoma is a rare malignancy. Due to late diagnosis and no adequate effective adjuvant treatment, prognosis remains poor. Only approximately 30% of these malignancies are confined to the adrenal gland when they are diagnosed, as these tumors tend to be found years after their genesis. Cardiac involvement of adrenal carcinoma is very rare. We report a rare case of a 7-year-old female with right adrenal cortical carcinoma, involving the right-side heart. |
format | Online Article Text |
id | pubmed-4963988 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Hindawi Publishing Corporation |
record_format | MEDLINE/PubMed |
spelling | pubmed-49639882016-08-04 Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach Iezzi, Federica Quarti, Andrea Surace, Chiara Pozzi, Marco Case Rep Cardiol Case Report Adrenocortical carcinoma is a rare malignancy. Due to late diagnosis and no adequate effective adjuvant treatment, prognosis remains poor. Only approximately 30% of these malignancies are confined to the adrenal gland when they are diagnosed, as these tumors tend to be found years after their genesis. Cardiac involvement of adrenal carcinoma is very rare. We report a rare case of a 7-year-old female with right adrenal cortical carcinoma, involving the right-side heart. Hindawi Publishing Corporation 2016 2016-07-14 /pmc/articles/PMC4963988/ /pubmed/27493811 http://dx.doi.org/10.1155/2016/2321017 Text en Copyright © 2016 Federica Iezzi et al. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Iezzi, Federica Quarti, Andrea Surace, Chiara Pozzi, Marco Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach |
title | Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach |
title_full | Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach |
title_fullStr | Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach |
title_full_unstemmed | Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach |
title_short | Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach |
title_sort | paediatric nonfunctioning adrenocortical carcinoma with extension up to right-side heart: cardiac surgery approach |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4963988/ https://www.ncbi.nlm.nih.gov/pubmed/27493811 http://dx.doi.org/10.1155/2016/2321017 |
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