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Pachydermodactyly – a report of two cases
Pachydermodactyly (PDD) is a rare and benign form of digital soft tissues fibromatosis, which affects the skin of the fingers. The disorder is characterized by asymptomatic, symmetric, progressive soft tissue swelling of the proximal interphalangeal (PIP) joints of the fingers. The etiology of disea...
Autores principales: | , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4967981/ https://www.ncbi.nlm.nih.gov/pubmed/27504024 http://dx.doi.org/10.5114/reum.2016.61215 |
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author | Żuber, Zbigniew Dyduch, Grzegorz Jaworek, Andrzej Turowska-Heydel, Dorota Sobczyk, Małgorzata Banach-Górnicka, Marta Rusnak, Katarzyna Górecki, Wojciech |
author_facet | Żuber, Zbigniew Dyduch, Grzegorz Jaworek, Andrzej Turowska-Heydel, Dorota Sobczyk, Małgorzata Banach-Górnicka, Marta Rusnak, Katarzyna Górecki, Wojciech |
author_sort | Żuber, Zbigniew |
collection | PubMed |
description | Pachydermodactyly (PDD) is a rare and benign form of digital soft tissues fibromatosis, which affects the skin of the fingers. The disorder is characterized by asymptomatic, symmetric, progressive soft tissue swelling of the proximal interphalangeal (PIP) joints of the fingers. The etiology of disease remains unknown. It is usually acquired, even though there are some publications that document family cases. It affects mainly adolescent men. We report two boys with the bilateral swelling of the of the PIP joints of the fingers and skin and subcutaneous tissue thickening. Based on clinical manifestations, radiological study and histopathological examination, pachydermodactyly was diagnosed. PDD is a rare and benign disorder, although it is important to consider other diseases, especially rheumatic conditions, in the differential diagnosis in order to avoid unnecessary additional tests and treatments. |
format | Online Article Text |
id | pubmed-4967981 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie |
record_format | MEDLINE/PubMed |
spelling | pubmed-49679812016-08-08 Pachydermodactyly – a report of two cases Żuber, Zbigniew Dyduch, Grzegorz Jaworek, Andrzej Turowska-Heydel, Dorota Sobczyk, Małgorzata Banach-Górnicka, Marta Rusnak, Katarzyna Górecki, Wojciech Reumatologia Case Report Pachydermodactyly (PDD) is a rare and benign form of digital soft tissues fibromatosis, which affects the skin of the fingers. The disorder is characterized by asymptomatic, symmetric, progressive soft tissue swelling of the proximal interphalangeal (PIP) joints of the fingers. The etiology of disease remains unknown. It is usually acquired, even though there are some publications that document family cases. It affects mainly adolescent men. We report two boys with the bilateral swelling of the of the PIP joints of the fingers and skin and subcutaneous tissue thickening. Based on clinical manifestations, radiological study and histopathological examination, pachydermodactyly was diagnosed. PDD is a rare and benign disorder, although it is important to consider other diseases, especially rheumatic conditions, in the differential diagnosis in order to avoid unnecessary additional tests and treatments. Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie 2016-07-18 2016 /pmc/articles/PMC4967981/ /pubmed/27504024 http://dx.doi.org/10.5114/reum.2016.61215 Text en Copyright © Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji w Warszawie 2016 http://creativecommons.org/licenses/by-nc-sa/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International (CC BY-NC-SA 4.0) License, allowing third parties to copy and redistribute the material in any medium or format and to remix, transform, and build upon the material, provided the original work is properly cited and states its license. |
spellingShingle | Case Report Żuber, Zbigniew Dyduch, Grzegorz Jaworek, Andrzej Turowska-Heydel, Dorota Sobczyk, Małgorzata Banach-Górnicka, Marta Rusnak, Katarzyna Górecki, Wojciech Pachydermodactyly – a report of two cases |
title | Pachydermodactyly – a report of two cases |
title_full | Pachydermodactyly – a report of two cases |
title_fullStr | Pachydermodactyly – a report of two cases |
title_full_unstemmed | Pachydermodactyly – a report of two cases |
title_short | Pachydermodactyly – a report of two cases |
title_sort | pachydermodactyly – a report of two cases |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4967981/ https://www.ncbi.nlm.nih.gov/pubmed/27504024 http://dx.doi.org/10.5114/reum.2016.61215 |
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