Long term follow up after resection emphasizes the role of surgery in Primary Hepatic Epithelioid Hemangioendothelioma

BACKGROUND: Primary Hepatic Epithelioid Hemangioendothelioma is an extremely rare tumor of vascular origin. PATIENTS: In this work we present clinical data and long term results of eight patients who were surgically treated in our institution. Liver transplantation was performed in five patients (fo...

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Detalles Bibliográficos
Autores principales: Mehrabi, Arianeb, Hoffmann, Katrin, Weiss, Karl Heinz, Mogler, Carolin, Schemmer, Peter, Büchler, Markus W., Alldinger, Ingo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2016
Materias:
Original Research
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4995439/
https://www.ncbi.nlm.nih.gov/pubmed/27594996
http://dx.doi.org/10.1016/j.amsu.2016.03.002
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author Mehrabi, Arianeb
Hoffmann, Katrin
Weiss, Karl Heinz
Mogler, Carolin
Schemmer, Peter
Büchler, Markus W.
Alldinger, Ingo
author_facet Mehrabi, Arianeb
Hoffmann, Katrin
Weiss, Karl Heinz
Mogler, Carolin
Schemmer, Peter
Büchler, Markus W.
Alldinger, Ingo
author_sort Mehrabi, Arianeb
collection PubMed
description BACKGROUND: Primary Hepatic Epithelioid Hemangioendothelioma is an extremely rare tumor of vascular origin. PATIENTS: In this work we present clinical data and long term results of eight patients who were surgically treated in our institution. Liver transplantation was performed in five patients (four cadaveric and one living related) and major liver resection in three patients. Three patients are alive with recurrent tumor. After a median follow-up of 100 months (48–266) all patients are alive. CONCLUSIONS: Only surgery can provide cure in HEH. If the extent of the disease prohibits primary resection liver transplantation might offer the most valuable option.
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spelling pubmed-49954392016-09-02 Long term follow up after resection emphasizes the role of surgery in Primary Hepatic Epithelioid Hemangioendothelioma Mehrabi, Arianeb Hoffmann, Katrin Weiss, Karl Heinz Mogler, Carolin Schemmer, Peter Büchler, Markus W. Alldinger, Ingo Ann Med Surg (Lond) Original Research BACKGROUND: Primary Hepatic Epithelioid Hemangioendothelioma is an extremely rare tumor of vascular origin. PATIENTS: In this work we present clinical data and long term results of eight patients who were surgically treated in our institution. Liver transplantation was performed in five patients (four cadaveric and one living related) and major liver resection in three patients. Three patients are alive with recurrent tumor. After a median follow-up of 100 months (48–266) all patients are alive. CONCLUSIONS: Only surgery can provide cure in HEH. If the extent of the disease prohibits primary resection liver transplantation might offer the most valuable option. Elsevier 2016-03-10 /pmc/articles/PMC4995439/ /pubmed/27594996 http://dx.doi.org/10.1016/j.amsu.2016.03.002 Text en © 2016 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Original Research
Mehrabi, Arianeb
Hoffmann, Katrin
Weiss, Karl Heinz
Mogler, Carolin
Schemmer, Peter
Büchler, Markus W.
Alldinger, Ingo
Long term follow up after resection emphasizes the role of surgery in Primary Hepatic Epithelioid Hemangioendothelioma
title Long term follow up after resection emphasizes the role of surgery in Primary Hepatic Epithelioid Hemangioendothelioma
title_full Long term follow up after resection emphasizes the role of surgery in Primary Hepatic Epithelioid Hemangioendothelioma
title_fullStr Long term follow up after resection emphasizes the role of surgery in Primary Hepatic Epithelioid Hemangioendothelioma
title_full_unstemmed Long term follow up after resection emphasizes the role of surgery in Primary Hepatic Epithelioid Hemangioendothelioma
title_short Long term follow up after resection emphasizes the role of surgery in Primary Hepatic Epithelioid Hemangioendothelioma
title_sort long term follow up after resection emphasizes the role of surgery in primary hepatic epithelioid hemangioendothelioma
topic Original Research
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4995439/
https://www.ncbi.nlm.nih.gov/pubmed/27594996
http://dx.doi.org/10.1016/j.amsu.2016.03.002
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