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Nutritional status of patients with phenylketonuria in Japan

Accumulating evidence suggests that hyperphenylalaninemia in phenylketonuria (PKU) can cause neuropsychological and psychosocial problems in diet-off adult patients, and that such symptoms improve after resumption of phenylalanine-restricted diet, indicating the need for lifetime low-phenylalanine d...

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Detalles Bibliográficos
Autores principales:	Okano, Yoshiyuki, Hattori, Toshikazu, Fujimoto, Hiroki, Noi, Kaori, Okamoto, Miki, Watanabe, Toshiaki, Watanabe, Ryoko, Fujii, Rika, Tamaoki, Tomoko
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Elsevier 2016
Materias:	Research Paper
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4995528/ https://www.ncbi.nlm.nih.gov/pubmed/27595068 http://dx.doi.org/10.1016/j.ymgmr.2016.08.005

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