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SLIRP stabilizes LRPPRC via an RRM–PPR protein interface

LRPPRC is a protein that has attracted interest both for its role in post-transcriptional regulation of mitochondrial gene expression and more recently because numerous mutated variants have been characterized as causing severe infantile mitochondrial neurodegeneration. LRPPRC belongs to the pentatr...

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Detalles Bibliográficos
Autores principales:	Spåhr, Henrik, Rozanska, Agata, Li, Xinping, Atanassov, Ilian, Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M. A., Rackham, Oliver, Larsson, Nils-Göran
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Oxford University Press 2016
Materias:	Molecular Biology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5001613/ https://www.ncbi.nlm.nih.gov/pubmed/27353330 http://dx.doi.org/10.1093/nar/gkw575

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