Cargando…

Neovascular glaucoma in a child: an unusual presentation of medulloepithelioma

A healthy 12 month old infant without significant medical history presented with left eye redness for one week. Ophthalmic examination showed elevated intraocular pressure with iris neovascularization in the affected eye with increased optic nerve cupping. Scleral depression revealed a ciliary body...

Descripción completa

Detalles Bibliográficos
Autores principales: Kassa, Enoch, Li, Helen, Sun, Yang
Formato: Online Artículo Texto
Lenguaje:English
Publicado: German Medical Science GMS Publishing House 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5015618/
https://www.ncbi.nlm.nih.gov/pubmed/27625938
http://dx.doi.org/10.3205/oc000016
_version_ 1782452470619832320
author Kassa, Enoch
Li, Helen
Sun, Yang
author_facet Kassa, Enoch
Li, Helen
Sun, Yang
author_sort Kassa, Enoch
collection PubMed
description A healthy 12 month old infant without significant medical history presented with left eye redness for one week. Ophthalmic examination showed elevated intraocular pressure with iris neovascularization in the affected eye with increased optic nerve cupping. Scleral depression revealed a ciliary body mass in the supratemporal quadrant. A large, non-pigmented, vascular mass was noted; biopsy results showed multilayered cords, tubules, and sheets resembling primitive medullary epithelium arising from the ciliary body. The patient was diagnosed with medulloepithelioma. The patient underwent enucleation of the affected eye. Medulloepithelioma is a rare but important cause of neovascular glaucoma in the pediatric population. This case will focus on the characteristics of medulloepthelioma and the differential diagnosis for a non-pigmented ciliary body mass in a child.
format Online
Article
Text
id pubmed-5015618
institution National Center for Biotechnology Information
language English
publishDate 2014
publisher German Medical Science GMS Publishing House
record_format MEDLINE/PubMed
spelling pubmed-50156182016-09-13 Neovascular glaucoma in a child: an unusual presentation of medulloepithelioma Kassa, Enoch Li, Helen Sun, Yang GMS Ophthalmol Cases Article A healthy 12 month old infant without significant medical history presented with left eye redness for one week. Ophthalmic examination showed elevated intraocular pressure with iris neovascularization in the affected eye with increased optic nerve cupping. Scleral depression revealed a ciliary body mass in the supratemporal quadrant. A large, non-pigmented, vascular mass was noted; biopsy results showed multilayered cords, tubules, and sheets resembling primitive medullary epithelium arising from the ciliary body. The patient was diagnosed with medulloepithelioma. The patient underwent enucleation of the affected eye. Medulloepithelioma is a rare but important cause of neovascular glaucoma in the pediatric population. This case will focus on the characteristics of medulloepthelioma and the differential diagnosis for a non-pigmented ciliary body mass in a child. German Medical Science GMS Publishing House 2014-04-17 /pmc/articles/PMC5015618/ /pubmed/27625938 http://dx.doi.org/10.3205/oc000016 Text en Copyright © 2014 Kassa et al. http://creativecommons.org/licenses/by-nc-nd/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution License. You are free: to Share – to copy, distribute and transmit the work, provided the original author and source are credited.
spellingShingle Article
Kassa, Enoch
Li, Helen
Sun, Yang
Neovascular glaucoma in a child: an unusual presentation of medulloepithelioma
title Neovascular glaucoma in a child: an unusual presentation of medulloepithelioma
title_full Neovascular glaucoma in a child: an unusual presentation of medulloepithelioma
title_fullStr Neovascular glaucoma in a child: an unusual presentation of medulloepithelioma
title_full_unstemmed Neovascular glaucoma in a child: an unusual presentation of medulloepithelioma
title_short Neovascular glaucoma in a child: an unusual presentation of medulloepithelioma
title_sort neovascular glaucoma in a child: an unusual presentation of medulloepithelioma
topic Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5015618/
https://www.ncbi.nlm.nih.gov/pubmed/27625938
http://dx.doi.org/10.3205/oc000016
work_keys_str_mv AT kassaenoch neovascularglaucomainachildanunusualpresentationofmedulloepithelioma
AT lihelen neovascularglaucomainachildanunusualpresentationofmedulloepithelioma
AT sunyang neovascularglaucomainachildanunusualpresentationofmedulloepithelioma