Nevoid Basal Cell Carcinoma Syndrome - Clinical and Radiological Findings of Three Cases

Nevoid basal cell carcinoma syndrome (NBCCS) is an autosomal dominant disorder, characterized by skeletal anomalies and multiple keratocystic odontogenic tumors of the jaws. The skeletal anomalies of this syndrome are mandibular prognathism, bossing of frontal and parietal bones, high-arched palate,...

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Detalles Bibliográficos
Autores principales: Ali, Ibrahim K, Karjodkar, Freny R, Sansare, Kaustubh, Salve, Prashant, Dora, Amaresh, Goyal, Shikha
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2016
Materias:
Radiology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5016041/
https://www.ncbi.nlm.nih.gov/pubmed/27630800
http://dx.doi.org/10.7759/cureus.727
Descripción
Sumario:Nevoid basal cell carcinoma syndrome (NBCCS) is an autosomal dominant disorder, characterized by skeletal anomalies and multiple keratocystic odontogenic tumors of the jaws. The skeletal anomalies of this syndrome are mandibular prognathism, bossing of frontal and parietal bones, high-arched palate, and bifid rib. We report three cases with NBCCS, emphasizing the clinical and radiographic findings, the importance of the early diagnosis of NBCCS, and a preventive multidisciplinary approach in the management of NBCCS.

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