Nevoid Basal Cell Carcinoma Syndrome - Clinical and Radiological Findings of Three Cases

Nevoid basal cell carcinoma syndrome (NBCCS) is an autosomal dominant disorder, characterized by skeletal anomalies and multiple keratocystic odontogenic tumors of the jaws. The skeletal anomalies of this syndrome are mandibular prognathism, bossing of frontal and parietal bones, high-arched palate,...

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Autores principales: Ali, Ibrahim K, Karjodkar, Freny R, Sansare, Kaustubh, Salve, Prashant, Dora, Amaresh, Goyal, Shikha
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2016
Materias:
Radiology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5016041/
https://www.ncbi.nlm.nih.gov/pubmed/27630800
http://dx.doi.org/10.7759/cureus.727
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author Ali, Ibrahim K
Karjodkar, Freny R
Sansare, Kaustubh
Salve, Prashant
Dora, Amaresh
Goyal, Shikha
author_facet Ali, Ibrahim K
Karjodkar, Freny R
Sansare, Kaustubh
Salve, Prashant
Dora, Amaresh
Goyal, Shikha
author_sort Ali, Ibrahim K
collection PubMed
description Nevoid basal cell carcinoma syndrome (NBCCS) is an autosomal dominant disorder, characterized by skeletal anomalies and multiple keratocystic odontogenic tumors of the jaws. The skeletal anomalies of this syndrome are mandibular prognathism, bossing of frontal and parietal bones, high-arched palate, and bifid rib. We report three cases with NBCCS, emphasizing the clinical and radiographic findings, the importance of the early diagnosis of NBCCS, and a preventive multidisciplinary approach in the management of NBCCS.
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spelling pubmed-50160412016-09-14 Nevoid Basal Cell Carcinoma Syndrome - Clinical and Radiological Findings of Three Cases Ali, Ibrahim K Karjodkar, Freny R Sansare, Kaustubh Salve, Prashant Dora, Amaresh Goyal, Shikha Cureus Radiology Nevoid basal cell carcinoma syndrome (NBCCS) is an autosomal dominant disorder, characterized by skeletal anomalies and multiple keratocystic odontogenic tumors of the jaws. The skeletal anomalies of this syndrome are mandibular prognathism, bossing of frontal and parietal bones, high-arched palate, and bifid rib. We report three cases with NBCCS, emphasizing the clinical and radiographic findings, the importance of the early diagnosis of NBCCS, and a preventive multidisciplinary approach in the management of NBCCS. Cureus 2016-08-08 /pmc/articles/PMC5016041/ /pubmed/27630800 http://dx.doi.org/10.7759/cureus.727 Text en Copyright © 2016, Ali et al. http://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Radiology
Ali, Ibrahim K
Karjodkar, Freny R
Sansare, Kaustubh
Salve, Prashant
Dora, Amaresh
Goyal, Shikha
Nevoid Basal Cell Carcinoma Syndrome - Clinical and Radiological Findings of Three Cases
title Nevoid Basal Cell Carcinoma Syndrome - Clinical and Radiological Findings of Three Cases
title_full Nevoid Basal Cell Carcinoma Syndrome - Clinical and Radiological Findings of Three Cases
title_fullStr Nevoid Basal Cell Carcinoma Syndrome - Clinical and Radiological Findings of Three Cases
title_full_unstemmed Nevoid Basal Cell Carcinoma Syndrome - Clinical and Radiological Findings of Three Cases
title_short Nevoid Basal Cell Carcinoma Syndrome - Clinical and Radiological Findings of Three Cases
title_sort nevoid basal cell carcinoma syndrome - clinical and radiological findings of three cases
topic Radiology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5016041/
https://www.ncbi.nlm.nih.gov/pubmed/27630800
http://dx.doi.org/10.7759/cureus.727
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