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Right posterior diaphragmatic hernia (Bochdalek) with liver involvement and alteration of hepatic outflow in adult: a case report

INTRODUCTION: Posterior right diaphragmatic hernia is rare in newborn patients but when present, is accompanied by high mortality. Pulmonary hypoplasia seems to be the main cause of death but the presence of liver involvement remains one of the reasons for poor prognosis even when intrauterine surge...

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Autores principales: Banchini, Filippo, Santoni, Roberta, Banchini, Antonio, Bodini, Flavio Cesare, Capelli, Patrizio
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Springer International Publishing 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5023639/
https://www.ncbi.nlm.nih.gov/pubmed/27652134
http://dx.doi.org/10.1186/s40064-016-3221-2
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author Banchini, Filippo
Santoni, Roberta
Banchini, Antonio
Bodini, Flavio Cesare
Capelli, Patrizio
author_facet Banchini, Filippo
Santoni, Roberta
Banchini, Antonio
Bodini, Flavio Cesare
Capelli, Patrizio
author_sort Banchini, Filippo
collection PubMed
description INTRODUCTION: Posterior right diaphragmatic hernia is rare in newborn patients but when present, is accompanied by high mortality. Pulmonary hypoplasia seems to be the main cause of death but the presence of liver involvement remains one of the reasons for poor prognosis even when intrauterine surgery is performed. CASE DESCRIPTION: In this article, we will present a rare case that was diagnosed by chance in a 65-year old adult presenting with an adenocarcinoma of the rectosigmoid junction and a right Bochdalek hernia with liver herniation and modification of the hepatic vein outflow with a natural right to left shunt. DISCUSSION: Diaphragmatic repair was performed on the patient with a mash and simultaneous colorectal resection. Intraoperatively, the exceptional natural modification of the hepatic outflow and alteration of the caval system was evident. CONCLUSION: This case report represent an extremely rare anatomic variation and could be useful to give new important information on the evolution that occur in foetal life.
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spelling pubmed-50236392016-09-20 Right posterior diaphragmatic hernia (Bochdalek) with liver involvement and alteration of hepatic outflow in adult: a case report Banchini, Filippo Santoni, Roberta Banchini, Antonio Bodini, Flavio Cesare Capelli, Patrizio Springerplus Case Study INTRODUCTION: Posterior right diaphragmatic hernia is rare in newborn patients but when present, is accompanied by high mortality. Pulmonary hypoplasia seems to be the main cause of death but the presence of liver involvement remains one of the reasons for poor prognosis even when intrauterine surgery is performed. CASE DESCRIPTION: In this article, we will present a rare case that was diagnosed by chance in a 65-year old adult presenting with an adenocarcinoma of the rectosigmoid junction and a right Bochdalek hernia with liver herniation and modification of the hepatic vein outflow with a natural right to left shunt. DISCUSSION: Diaphragmatic repair was performed on the patient with a mash and simultaneous colorectal resection. Intraoperatively, the exceptional natural modification of the hepatic outflow and alteration of the caval system was evident. CONCLUSION: This case report represent an extremely rare anatomic variation and could be useful to give new important information on the evolution that occur in foetal life. Springer International Publishing 2016-09-14 /pmc/articles/PMC5023639/ /pubmed/27652134 http://dx.doi.org/10.1186/s40064-016-3221-2 Text en © The Author(s) 2016 Open AccessThis article is distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made.
spellingShingle Case Study
Banchini, Filippo
Santoni, Roberta
Banchini, Antonio
Bodini, Flavio Cesare
Capelli, Patrizio
Right posterior diaphragmatic hernia (Bochdalek) with liver involvement and alteration of hepatic outflow in adult: a case report
title Right posterior diaphragmatic hernia (Bochdalek) with liver involvement and alteration of hepatic outflow in adult: a case report
title_full Right posterior diaphragmatic hernia (Bochdalek) with liver involvement and alteration of hepatic outflow in adult: a case report
title_fullStr Right posterior diaphragmatic hernia (Bochdalek) with liver involvement and alteration of hepatic outflow in adult: a case report
title_full_unstemmed Right posterior diaphragmatic hernia (Bochdalek) with liver involvement and alteration of hepatic outflow in adult: a case report
title_short Right posterior diaphragmatic hernia (Bochdalek) with liver involvement and alteration of hepatic outflow in adult: a case report
title_sort right posterior diaphragmatic hernia (bochdalek) with liver involvement and alteration of hepatic outflow in adult: a case report
topic Case Study
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5023639/
https://www.ncbi.nlm.nih.gov/pubmed/27652134
http://dx.doi.org/10.1186/s40064-016-3221-2
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