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Synovial sarcoma of the hypopharynx in a pediatric patient: Case report

INTRODUCTION: Synovial sarcoma (SS) is uncommon high grade soft tissue sarcoma, accounting for less than 10% of all head and neck sarcomas. Also, about 10% of SS occur within the Head & Neck. In the pediatric population, SS is an extremely rare head & neck malignancy. PRESENTATION OF CASE: W...

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Autores principales: Alotaibi, N.H., Bornand, Aurélie, Dulguerov, Nicolas, Becker, M., Dulguerov, Pavel
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5031474/
https://www.ncbi.nlm.nih.gov/pubmed/27649458
http://dx.doi.org/10.1016/j.ijscr.2016.08.043
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author Alotaibi, N.H.
Bornand, Aurélie
Dulguerov, Nicolas
Becker, M.
Dulguerov, Pavel
author_facet Alotaibi, N.H.
Bornand, Aurélie
Dulguerov, Nicolas
Becker, M.
Dulguerov, Pavel
author_sort Alotaibi, N.H.
collection PubMed
description INTRODUCTION: Synovial sarcoma (SS) is uncommon high grade soft tissue sarcoma, accounting for less than 10% of all head and neck sarcomas. Also, about 10% of SS occur within the Head & Neck. In the pediatric population, SS is an extremely rare head & neck malignancy. PRESENTATION OF CASE: We present a case of sixteen years old boy diagnosed with SS situated of the hypopharynx treated by surgical excision and post operative radio-chemotherapy. DISCUSSION: This anatomical location brings additional functional challenges (swallowing, phonation, respiration), especially in the pediatric population. Pre-operative and even post-operative histopathological diagnosis of SS remains difficult. Optimal treatment of Head & Neck SS has to balance functional and oncologic aspects. CONCLUSION: SS is an extremely rare head & neck malignancy in pediatric population. It has multifaceted challenges including pre and post-operative histopathological diagnosis and optimal modality of treatment. Clinical judgment, especially in the pediatric population, needs to balance tumor free margins and organ preservation in head and neck region.
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spelling pubmed-50314742016-09-29 Synovial sarcoma of the hypopharynx in a pediatric patient: Case report Alotaibi, N.H. Bornand, Aurélie Dulguerov, Nicolas Becker, M. Dulguerov, Pavel Int J Surg Case Rep Case Report INTRODUCTION: Synovial sarcoma (SS) is uncommon high grade soft tissue sarcoma, accounting for less than 10% of all head and neck sarcomas. Also, about 10% of SS occur within the Head & Neck. In the pediatric population, SS is an extremely rare head & neck malignancy. PRESENTATION OF CASE: We present a case of sixteen years old boy diagnosed with SS situated of the hypopharynx treated by surgical excision and post operative radio-chemotherapy. DISCUSSION: This anatomical location brings additional functional challenges (swallowing, phonation, respiration), especially in the pediatric population. Pre-operative and even post-operative histopathological diagnosis of SS remains difficult. Optimal treatment of Head & Neck SS has to balance functional and oncologic aspects. CONCLUSION: SS is an extremely rare head & neck malignancy in pediatric population. It has multifaceted challenges including pre and post-operative histopathological diagnosis and optimal modality of treatment. Clinical judgment, especially in the pediatric population, needs to balance tumor free margins and organ preservation in head and neck region. Elsevier 2016-09-03 /pmc/articles/PMC5031474/ /pubmed/27649458 http://dx.doi.org/10.1016/j.ijscr.2016.08.043 Text en © 2016 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Alotaibi, N.H.
Bornand, Aurélie
Dulguerov, Nicolas
Becker, M.
Dulguerov, Pavel
Synovial sarcoma of the hypopharynx in a pediatric patient: Case report
title Synovial sarcoma of the hypopharynx in a pediatric patient: Case report
title_full Synovial sarcoma of the hypopharynx in a pediatric patient: Case report
title_fullStr Synovial sarcoma of the hypopharynx in a pediatric patient: Case report
title_full_unstemmed Synovial sarcoma of the hypopharynx in a pediatric patient: Case report
title_short Synovial sarcoma of the hypopharynx in a pediatric patient: Case report
title_sort synovial sarcoma of the hypopharynx in a pediatric patient: case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5031474/
https://www.ncbi.nlm.nih.gov/pubmed/27649458
http://dx.doi.org/10.1016/j.ijscr.2016.08.043
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