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Synovial sarcoma of the hypopharynx in a pediatric patient: Case report
INTRODUCTION: Synovial sarcoma (SS) is uncommon high grade soft tissue sarcoma, accounting for less than 10% of all head and neck sarcomas. Also, about 10% of SS occur within the Head & Neck. In the pediatric population, SS is an extremely rare head & neck malignancy. PRESENTATION OF CASE: W...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5031474/ https://www.ncbi.nlm.nih.gov/pubmed/27649458 http://dx.doi.org/10.1016/j.ijscr.2016.08.043 |
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author | Alotaibi, N.H. Bornand, Aurélie Dulguerov, Nicolas Becker, M. Dulguerov, Pavel |
author_facet | Alotaibi, N.H. Bornand, Aurélie Dulguerov, Nicolas Becker, M. Dulguerov, Pavel |
author_sort | Alotaibi, N.H. |
collection | PubMed |
description | INTRODUCTION: Synovial sarcoma (SS) is uncommon high grade soft tissue sarcoma, accounting for less than 10% of all head and neck sarcomas. Also, about 10% of SS occur within the Head & Neck. In the pediatric population, SS is an extremely rare head & neck malignancy. PRESENTATION OF CASE: We present a case of sixteen years old boy diagnosed with SS situated of the hypopharynx treated by surgical excision and post operative radio-chemotherapy. DISCUSSION: This anatomical location brings additional functional challenges (swallowing, phonation, respiration), especially in the pediatric population. Pre-operative and even post-operative histopathological diagnosis of SS remains difficult. Optimal treatment of Head & Neck SS has to balance functional and oncologic aspects. CONCLUSION: SS is an extremely rare head & neck malignancy in pediatric population. It has multifaceted challenges including pre and post-operative histopathological diagnosis and optimal modality of treatment. Clinical judgment, especially in the pediatric population, needs to balance tumor free margins and organ preservation in head and neck region. |
format | Online Article Text |
id | pubmed-5031474 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Elsevier |
record_format | MEDLINE/PubMed |
spelling | pubmed-50314742016-09-29 Synovial sarcoma of the hypopharynx in a pediatric patient: Case report Alotaibi, N.H. Bornand, Aurélie Dulguerov, Nicolas Becker, M. Dulguerov, Pavel Int J Surg Case Rep Case Report INTRODUCTION: Synovial sarcoma (SS) is uncommon high grade soft tissue sarcoma, accounting for less than 10% of all head and neck sarcomas. Also, about 10% of SS occur within the Head & Neck. In the pediatric population, SS is an extremely rare head & neck malignancy. PRESENTATION OF CASE: We present a case of sixteen years old boy diagnosed with SS situated of the hypopharynx treated by surgical excision and post operative radio-chemotherapy. DISCUSSION: This anatomical location brings additional functional challenges (swallowing, phonation, respiration), especially in the pediatric population. Pre-operative and even post-operative histopathological diagnosis of SS remains difficult. Optimal treatment of Head & Neck SS has to balance functional and oncologic aspects. CONCLUSION: SS is an extremely rare head & neck malignancy in pediatric population. It has multifaceted challenges including pre and post-operative histopathological diagnosis and optimal modality of treatment. Clinical judgment, especially in the pediatric population, needs to balance tumor free margins and organ preservation in head and neck region. Elsevier 2016-09-03 /pmc/articles/PMC5031474/ /pubmed/27649458 http://dx.doi.org/10.1016/j.ijscr.2016.08.043 Text en © 2016 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Case Report Alotaibi, N.H. Bornand, Aurélie Dulguerov, Nicolas Becker, M. Dulguerov, Pavel Synovial sarcoma of the hypopharynx in a pediatric patient: Case report |
title | Synovial sarcoma of the hypopharynx in a pediatric patient: Case report |
title_full | Synovial sarcoma of the hypopharynx in a pediatric patient: Case report |
title_fullStr | Synovial sarcoma of the hypopharynx in a pediatric patient: Case report |
title_full_unstemmed | Synovial sarcoma of the hypopharynx in a pediatric patient: Case report |
title_short | Synovial sarcoma of the hypopharynx in a pediatric patient: Case report |
title_sort | synovial sarcoma of the hypopharynx in a pediatric patient: case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5031474/ https://www.ncbi.nlm.nih.gov/pubmed/27649458 http://dx.doi.org/10.1016/j.ijscr.2016.08.043 |
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