A rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus

Eosinophilic fasciitis, also known as Shulman's syndrome, is a fibrosing scleroderma-like syndrome, which is a distinct entity. A 55-year-old man, presented with progressive skin darkening, thickening, and tightening over the left lower limb since 6 months. Dermatological examination revealed a...

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Autores principales: Sharma, Aseem, Ray, Rahul, Sridhar, Jandhyala, Trehan, Arti, Khandare, Manish
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2016
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5038099/
https://www.ncbi.nlm.nih.gov/pubmed/27730034
http://dx.doi.org/10.4103/2229-5178.190516
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author Sharma, Aseem
Ray, Rahul
Sridhar, Jandhyala
Trehan, Arti
Khandare, Manish
author_facet Sharma, Aseem
Ray, Rahul
Sridhar, Jandhyala
Trehan, Arti
Khandare, Manish
author_sort Sharma, Aseem
collection PubMed
description Eosinophilic fasciitis, also known as Shulman's syndrome, is a fibrosing scleroderma-like syndrome, which is a distinct entity. A 55-year-old man, presented with progressive skin darkening, thickening, and tightening over the left lower limb since 6 months. Dermatological examination revealed a hyperpigmented indurated area on the left thigh, extending to the anterior aspect of the left leg. A well-defined hypopigmented indurated plaque was present over the left iliac region. Histopathology and imaging studies confirmed the diagnosis of eosinophilic fasciitis and lichen sclerosus. The indurated lesion on the left lower limb responded dramatically well to oral corticosteroids. This is a rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus.
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spelling pubmed-50380992016-10-11 A rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus Sharma, Aseem Ray, Rahul Sridhar, Jandhyala Trehan, Arti Khandare, Manish Indian Dermatol Online J Case Report Eosinophilic fasciitis, also known as Shulman's syndrome, is a fibrosing scleroderma-like syndrome, which is a distinct entity. A 55-year-old man, presented with progressive skin darkening, thickening, and tightening over the left lower limb since 6 months. Dermatological examination revealed a hyperpigmented indurated area on the left thigh, extending to the anterior aspect of the left leg. A well-defined hypopigmented indurated plaque was present over the left iliac region. Histopathology and imaging studies confirmed the diagnosis of eosinophilic fasciitis and lichen sclerosus. The indurated lesion on the left lower limb responded dramatically well to oral corticosteroids. This is a rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus. Medknow Publications & Media Pvt Ltd 2016 /pmc/articles/PMC5038099/ /pubmed/27730034 http://dx.doi.org/10.4103/2229-5178.190516 Text en Copyright: © Indian Dermatology Online Journal http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
spellingShingle Case Report
Sharma, Aseem
Ray, Rahul
Sridhar, Jandhyala
Trehan, Arti
Khandare, Manish
A rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus
title A rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus
title_full A rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus
title_fullStr A rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus
title_full_unstemmed A rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus
title_short A rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus
title_sort rare case of unilateral eosinophilic fasciitis associated with ipsilateral extragenital lichen sclerosus
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5038099/
https://www.ncbi.nlm.nih.gov/pubmed/27730034
http://dx.doi.org/10.4103/2229-5178.190516
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