Primary umbilical endometriosis: A painful swelling in the umbilicus concomitantly with menstruation

BACKGROUND: Primary umblikal endometriosis is a rare illness. In this report we aimed to discuss the management of this rare condition. CASE SUMMARY: A 28-year-old nulliparous woman was present at our clinic who was suffering from painful swelling in the umbilicus during her menstruation for the last 3 months. Her examination showed a dark-color sensitive nodule of 20 × 15 mm in size in the umbilicus. A lower abdominal tomography was performed to exclude the presence of a concomitant pelvic endometriosis, and it showed increased density consistent with subcutaneous inflammation in the umbilicus. Her medical history and physical examination suggested primary umbilical endometriosis. A total resection including umbilicus was performed. DISCUSSION: Primary umbilical endometriosis is a rare benign disease and clinically difficult to differentiate from other diseases that cause umbilical nodule. Imaging modalities have no pathognomonic findings for diagnosis. Surgical exploration and excision are the definitive and safe treatment of primary umbilical endometriosis. CONCLUSION: Total umbilical resection should be preferred to avoid local recurrent.