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Positive Impact of Eculizumab Therapy on Surgery for Budd-Chiari Syndrome in a Patient with Paroxysmal Nocturnal Hemoglobinuria and a Long-Term History of Thrombosis

Paroxysmal nocturnal hemoglobinuria (PNH) is associated with severe end-organ damage and a high risk of thrombosis. Budd-Chiari syndrome, which develops after thrombotic occlusion of major hepatic blood vessels, is relatively common in PNH and has been associated with increased mortality. We report...

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Detalles Bibliográficos
Autores principales: De-la-Iglesia, Silvia, Luzardo, Hugo, Lemes, Angelina, Torres, Melissa, Gómez-Casares, Maria Teresa, Cruz, Naylen, Molero, Teresa
Formato: Online Artículo Texto
Lenguaje:English
Publicado: PAGEPress Publications, Pavia, Italy 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5062621/
https://www.ncbi.nlm.nih.gov/pubmed/27757214
http://dx.doi.org/10.4081/hr.2016.6562