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Pedunculated Nodules as a Variant of Dermatofibrosarcoma Protuberans
Dermatofibrosarcoma protuberans (DFSP) is a rare disease of dermal fibroblastic origin that accounts for less than 5% of all soft tissue sarcomas in adults. DFSP grows slowly and is an asymptomatic lesion at the initial diagnosis. Herein, we report a case of multiple pedunculated nodules as a varian...
Autores principales: | , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Korean Dermatological Association; The Korean Society for Investigative Dermatology
2016
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5064194/ https://www.ncbi.nlm.nih.gov/pubmed/27746644 http://dx.doi.org/10.5021/ad.2016.28.5.629 |
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author | Kim, Min Jung Hur, Min Seok Choi, Byung Gon Kim, Soo Young Lee, Yang Won Choe, Yong Beom Ahn, Kyu Joong |
author_facet | Kim, Min Jung Hur, Min Seok Choi, Byung Gon Kim, Soo Young Lee, Yang Won Choe, Yong Beom Ahn, Kyu Joong |
author_sort | Kim, Min Jung |
collection | PubMed |
description | Dermatofibrosarcoma protuberans (DFSP) is a rare disease of dermal fibroblastic origin that accounts for less than 5% of all soft tissue sarcomas in adults. DFSP grows slowly and is an asymptomatic lesion at the initial diagnosis. Herein, we report a case of multiple pedunculated nodules as a variant of DFSP. A 47-year-old man presented with a 7-month history of multiple well-circumscribed, firm, pedunculated nodules on the inguinal area. Histopathologic examination results showed densely packed uniform spindle cells with a storiform and cartwheel pattern, and positivity for CD34. Wide excision and skin graft were performed and at the 6-month follow-up, there was no evidence of recurrence or metastasis. |
format | Online Article Text |
id | pubmed-5064194 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2016 |
publisher | Korean Dermatological Association; The Korean Society for Investigative Dermatology |
record_format | MEDLINE/PubMed |
spelling | pubmed-50641942016-10-14 Pedunculated Nodules as a Variant of Dermatofibrosarcoma Protuberans Kim, Min Jung Hur, Min Seok Choi, Byung Gon Kim, Soo Young Lee, Yang Won Choe, Yong Beom Ahn, Kyu Joong Ann Dermatol Case Report Dermatofibrosarcoma protuberans (DFSP) is a rare disease of dermal fibroblastic origin that accounts for less than 5% of all soft tissue sarcomas in adults. DFSP grows slowly and is an asymptomatic lesion at the initial diagnosis. Herein, we report a case of multiple pedunculated nodules as a variant of DFSP. A 47-year-old man presented with a 7-month history of multiple well-circumscribed, firm, pedunculated nodules on the inguinal area. Histopathologic examination results showed densely packed uniform spindle cells with a storiform and cartwheel pattern, and positivity for CD34. Wide excision and skin graft were performed and at the 6-month follow-up, there was no evidence of recurrence or metastasis. Korean Dermatological Association; The Korean Society for Investigative Dermatology 2016-10 2016-09-30 /pmc/articles/PMC5064194/ /pubmed/27746644 http://dx.doi.org/10.5021/ad.2016.28.5.629 Text en Copyright © 2016 The Korean Dermatological Association and The Korean Society for Investigative Dermatology http://creativecommons.org/licenses/by-nc/4.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Kim, Min Jung Hur, Min Seok Choi, Byung Gon Kim, Soo Young Lee, Yang Won Choe, Yong Beom Ahn, Kyu Joong Pedunculated Nodules as a Variant of Dermatofibrosarcoma Protuberans |
title | Pedunculated Nodules as a Variant of Dermatofibrosarcoma Protuberans |
title_full | Pedunculated Nodules as a Variant of Dermatofibrosarcoma Protuberans |
title_fullStr | Pedunculated Nodules as a Variant of Dermatofibrosarcoma Protuberans |
title_full_unstemmed | Pedunculated Nodules as a Variant of Dermatofibrosarcoma Protuberans |
title_short | Pedunculated Nodules as a Variant of Dermatofibrosarcoma Protuberans |
title_sort | pedunculated nodules as a variant of dermatofibrosarcoma protuberans |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5064194/ https://www.ncbi.nlm.nih.gov/pubmed/27746644 http://dx.doi.org/10.5021/ad.2016.28.5.629 |
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